FATAL LACTIC-ACIDOSIS DUE TO DEFICIENCY OF E1 COMPONENT OF THE PYRUVATE-DEHYDROGENASE COMPLEX

被引：9

作者：

BIRCHMACHIN, MA

SHEPHERD, IM

SOLOMON, M

YEAMAN, SJ

GARDNERMEDWIN, D

SHERRATT, HSA

LINDSAY, JG

AYNSLEYGREEN, A

TURNBULL, DM

机构：

[1] UNIV GLASGOW, DEPT BIOCHEM, GLASGOW G12 8QQ, SCOTLAND

[2] UNIV NEWCASTLE UPON TYNE, DEPT PHARMACOL SCI, NEWCASTLE UPON TYNE NE2 4HH, ENGLAND

[3] UNIV NEWCASTLE UPON TYNE, DEPT BIOCHEM, NEWCASTLE UPON TYNE NE2 4HH, ENGLAND

[4] UNIV NEWCASTLE UPON TYNE, DEPT CHILD HLTH, NEWCASTLE UPON TYNE NE2 4HH, ENGLAND

来源：

JOURNAL OF INHERITED METABOLIC DISEASE | 1988年 / 11卷 / 02期

关键词：

D O I：

10.1007/BF01799876

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

引用

页码：207 / 217

页数：11

共 23 条

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