DEFECT IN HURLERS AND HUNTERS SYNDROMES - FAULTY DEGRADATION OF MUCOPOLYSACCHARIDE

被引:353
作者
FRATANTONI, JC
HALL, CW
NEUFELD, EF
机构
关键词
D O I
10.1073/pnas.60.2.699
中图分类号
O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];
学科分类号
07 ; 0710 ; 09 ;
摘要
[No abstract available]
引用
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页码:699 / +
页数:1
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共 29 条
[21]  
MCKUSICK VA, 1966, HEREDITARY DISORDERS
[22]  
NEUFELD EF, 1966, METHODS ENZYMOLOG ED, V8, P53
[23]  
RODEN L, 1967, 7 INT C BIOCH TOK AB, V1, P69
[25]  
STANBURY JB, 1966, METABOLIC BASIS I ED, P963
[26]  
SUZUKI S, 1967, 7 INT C BIOCH, V4, P704
[27]   BIOSYNTHESIS OF CHONDROITIN-SULFATE PROTEIN COMPLEX [J].
TELSER, A ;
ROBINSON, HC ;
DORFMAN, A .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1965, 54 (03) :912-&
[28]  
TUDBALL N, 1967, FED PROC, V26, P856
[29]  
VANHOOF F, 1964, CR HEBD ACAD SCI, V259, P1281