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X-LINKED ADRENOLEUKODYSTROPHY - DEFECTIVE PEROXISOMAL OXIDATION OF VERY LONG-CHAIN FATTY-ACIDS BUT NOT OF VERY LONG-CHAIN FATTY ACYL-COA ESTERS

被引：58
作者：
WANDERS, RJA
VANROERMUND, CWT
VANWIJLAND, MJA
NIJENHUIS, AA
TROMP, A
SCHUTGENS, RBH
BROUWERKELDER, EM
SCHRAM, AW
TAGER, JM
VANDENBOSCH, H
SCHALKWIJK, C
机构：
[1] UNIV AMSTERDAM,ACAD MED CTR,DEPT PAEDIAT,1105 AZ AMSTERDAM,NETHERLANDS
[2] UNIV AMSTERDAM,ACAD MED CTR,DEPT CLIN CHEM,1105 AZ AMSTERDAM,NETHERLANDS
[3] UNIV AMSTERDAM,ACAD MED CTR,BIOCHEM LAB,1105 AZ AMSTERDAM,NETHERLANDS
[4] STATE UNIV UTRECHT,BIOCHEM LAB,UTRECHT,NETHERLANDS
来源：
CLINICA CHIMICA ACTA | 1987年 / 165卷 / 2-3期
关键词：
D O I：
10.1016/0009-8981(87)90177-X
中图分类号：
R446 [实验室诊断]; R-33 [实验医学、医学实验];
学科分类号：
1001 ;
摘要：
引用
收藏
页码：321 / 329
页数：9
相关论文
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