ENHANCED PROTEOLYTIC DEGRADATION OF NORMAL BETA-GALACTOSIDASE IN THE LYSOSOMAL STORAGE DISEASE WITH COMBINED BETA-GALACTOSIDASE AND NEURAMINIDASE DEFICIENCY

被引：51

作者：

VANDIGGELEN, OP ^{[1
]}

HOOGEVEEN, AT ^{[1
]}

SMITH, PJ ^{[1
]}

REUSER, AJJ ^{[1
]}

GALJAARD, H ^{[1
]}

机构：

[1] UNIV BRISTOL, DEPT ORGAN CHEM, BRISTOL BS8 1TS, AVON, ENGLAND

来源：

BIOCHIMICA ET BIOPHYSICA ACTA | 1982年 / 703卷 / 01期

关键词：

D O I：

10.1016/0167-4838(82)90012-7

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：69 / 76

页数：8

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