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SPECTROPHOTOMETRIC AND FLUORIMETRIC ASSAYS OF GALACTOCEREBROSIDASE ACTIVITY, THEIR USE IN THE DIAGNOSIS OF KRABBES DISEASE
被引:30
作者
:
BESLEY, GTN
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV EDINBURGH,EDINBURGH EH8 9YL,MIDLOTHIAN,SCOTLAND
BESLEY, GTN
GATT, S
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV EDINBURGH,EDINBURGH EH8 9YL,MIDLOTHIAN,SCOTLAND
GATT, S
机构
:
[1]
UNIV EDINBURGH,EDINBURGH EH8 9YL,MIDLOTHIAN,SCOTLAND
[2]
HEBREW UNIV JERUSALEM,HADASSAH HOSP & MED SCH,DEPT BIOCHEM,NEUROCHEM LAB,JERUSALEM,ISRAEL
来源
:
CLINICA CHIMICA ACTA
|
1981年
/ 110卷
/ 01期
关键词
:
D O I
:
10.1016/0009-8981(81)90295-3
中图分类号
:
R446 [实验室诊断];
R-33 [实验医学、医学实验];
学科分类号
:
1001 ;
摘要
:
引用
收藏
页码:19 / 26
页数:8
相关论文
共 14 条
[1]
KRABBES GLOBOID-CELL LEUCODYSTROPHY - STUDIES ON GALACTOSYLCERAMIDE BETA-GALACTOSIDASE AND NONSPECIFIC BETA-GALACTOSIDASE OF LEUKOCYTES, CULTURED SKIN FIBROBLASTS, AND AMNIOTIC-FLUID CELLS
BESLEY, GTN
论文数:
0
引用数:
0
h-index:
0
机构:
ROY HOSP SICK CHILDREN,DEPT PATHOL,EDINBURGH EH9 1LF,SCOTLAND
BESLEY, GTN
BAIN, AD
论文数:
0
引用数:
0
h-index:
0
机构:
ROY HOSP SICK CHILDREN,DEPT PATHOL,EDINBURGH EH9 1LF,SCOTLAND
BAIN, AD
[J].
JOURNAL OF MEDICAL GENETICS,
1976,
13
(03)
: 195
-
199
[2]
USE OF A CHROMOGENIC SUBSTRATE FOR DIAGNOSIS OF KRABBES DISEASE, WITH SPECIAL REFERENCE TO ITS APPLICATION IN PRENATAL DIAGNOSIS
BESLEY, GTN
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV EDINBURGH,EDINBURGH EH9 1LF,SCOTLAND
UNIV EDINBURGH,EDINBURGH EH9 1LF,SCOTLAND
BESLEY, GTN
BAIN, AD
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV EDINBURGH,EDINBURGH EH9 1LF,SCOTLAND
UNIV EDINBURGH,EDINBURGH EH9 1LF,SCOTLAND
BAIN, AD
[J].
CLINICA CHIMICA ACTA,
1978,
88
(02)
: 229
-
236
[3]
BESLEY GTN, METHODS ENZYMOLOGY D, V72
[4]
DOLE VP, 1956, J CLIN INVEST, V35, P350
[5]
PRACTICAL CHROMOGENIC PROCEDURE FOR DIAGNOSIS OF KRABBES DISEASE
GAL, AE
论文数:
0
引用数:
0
h-index:
0
机构:
NINCDS,DEV & METAB NEUROL BRANCH,BETHESDA,MD 20014
GAL, AE
BRADY, RO
论文数:
0
引用数:
0
h-index:
0
机构:
NINCDS,DEV & METAB NEUROL BRANCH,BETHESDA,MD 20014
BRADY, RO
PENTCHEV, PG
论文数:
0
引用数:
0
h-index:
0
机构:
NINCDS,DEV & METAB NEUROL BRANCH,BETHESDA,MD 20014
PENTCHEV, PG
FURBISH, FS
论文数:
0
引用数:
0
h-index:
0
机构:
NINCDS,DEV & METAB NEUROL BRANCH,BETHESDA,MD 20014
FURBISH, FS
SUZUKI, K
论文数:
0
引用数:
0
h-index:
0
机构:
NINCDS,DEV & METAB NEUROL BRANCH,BETHESDA,MD 20014
SUZUKI, K
TANAKA, H
论文数:
0
引用数:
0
h-index:
0
机构:
NINCDS,DEV & METAB NEUROL BRANCH,BETHESDA,MD 20014
TANAKA, H
SCHNEIDER, EL
论文数:
0
引用数:
0
h-index:
0
机构:
NINCDS,DEV & METAB NEUROL BRANCH,BETHESDA,MD 20014
SCHNEIDER, EL
[J].
CLINICA CHIMICA ACTA,
1977,
77
(01)
: 53
-
59
[6]
SPECTROPHOTOMETRIC METHOD FOR DETERMINATION OF SPHINGOMYELINASE
GATT, S
论文数:
0
引用数:
0
h-index:
0
GATT, S
DINUR, T
论文数:
0
引用数:
0
h-index:
0
DINUR, T
BARENHOLZ, Y
论文数:
0
引用数:
0
h-index:
0
BARENHOLZ, Y
[J].
BIOCHIMICA ET BIOPHYSICA ACTA,
1978,
530
(03)
: 503
-
507
[7]
GATT S, 1980, CLIN CHEM, V26, P93
[8]
SYNTHESIS OF TRINITROPHENYLAMINOLAURIC ACID AND USE OF ITS GLYCERYL ESTERS FOR ASSAYING LIPASE BY A SPECTROPHOTOMETRIC PROCEDURE
GOLDBERG, R
论文数:
0
引用数:
0
h-index:
0
机构:
HEBREW UNIV JERUSALEM,HADASSAH MED SCH,DEPT BIOCHEM,NEUROCHEM LAB,JERUSALEM 91000,ISRAEL
HEBREW UNIV JERUSALEM,HADASSAH MED SCH,DEPT BIOCHEM,NEUROCHEM LAB,JERUSALEM 91000,ISRAEL
GOLDBERG, R
BARENHOLZ, Y
论文数:
0
引用数:
0
h-index:
0
机构:
HEBREW UNIV JERUSALEM,HADASSAH MED SCH,DEPT BIOCHEM,NEUROCHEM LAB,JERUSALEM 91000,ISRAEL
HEBREW UNIV JERUSALEM,HADASSAH MED SCH,DEPT BIOCHEM,NEUROCHEM LAB,JERUSALEM 91000,ISRAEL
BARENHOLZ, Y
GATT, S
论文数:
0
引用数:
0
h-index:
0
机构:
HEBREW UNIV JERUSALEM,HADASSAH MED SCH,DEPT BIOCHEM,NEUROCHEM LAB,JERUSALEM 91000,ISRAEL
HEBREW UNIV JERUSALEM,HADASSAH MED SCH,DEPT BIOCHEM,NEUROCHEM LAB,JERUSALEM 91000,ISRAEL
GATT, S
[J].
BIOCHIMICA ET BIOPHYSICA ACTA,
1978,
531
(02)
: 237
-
241
[9]
HAMMARSTROM S, 1971, J LIPID RES, V12, P760
[10]
LOWRY OH, 1951, J BIOL CHEM, V193, P265
←
1
2
→
共 14 条
[1]
KRABBES GLOBOID-CELL LEUCODYSTROPHY - STUDIES ON GALACTOSYLCERAMIDE BETA-GALACTOSIDASE AND NONSPECIFIC BETA-GALACTOSIDASE OF LEUKOCYTES, CULTURED SKIN FIBROBLASTS, AND AMNIOTIC-FLUID CELLS
BESLEY, GTN
论文数:
0
引用数:
0
h-index:
0
机构:
ROY HOSP SICK CHILDREN,DEPT PATHOL,EDINBURGH EH9 1LF,SCOTLAND
BESLEY, GTN
BAIN, AD
论文数:
0
引用数:
0
h-index:
0
机构:
ROY HOSP SICK CHILDREN,DEPT PATHOL,EDINBURGH EH9 1LF,SCOTLAND
BAIN, AD
[J].
JOURNAL OF MEDICAL GENETICS,
1976,
13
(03)
: 195
-
199
[2]
USE OF A CHROMOGENIC SUBSTRATE FOR DIAGNOSIS OF KRABBES DISEASE, WITH SPECIAL REFERENCE TO ITS APPLICATION IN PRENATAL DIAGNOSIS
BESLEY, GTN
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV EDINBURGH,EDINBURGH EH9 1LF,SCOTLAND
UNIV EDINBURGH,EDINBURGH EH9 1LF,SCOTLAND
BESLEY, GTN
BAIN, AD
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV EDINBURGH,EDINBURGH EH9 1LF,SCOTLAND
UNIV EDINBURGH,EDINBURGH EH9 1LF,SCOTLAND
BAIN, AD
[J].
CLINICA CHIMICA ACTA,
1978,
88
(02)
: 229
-
236
[3]
BESLEY GTN, METHODS ENZYMOLOGY D, V72
[4]
DOLE VP, 1956, J CLIN INVEST, V35, P350
[5]
PRACTICAL CHROMOGENIC PROCEDURE FOR DIAGNOSIS OF KRABBES DISEASE
GAL, AE
论文数:
0
引用数:
0
h-index:
0
机构:
NINCDS,DEV & METAB NEUROL BRANCH,BETHESDA,MD 20014
GAL, AE
BRADY, RO
论文数:
0
引用数:
0
h-index:
0
机构:
NINCDS,DEV & METAB NEUROL BRANCH,BETHESDA,MD 20014
BRADY, RO
PENTCHEV, PG
论文数:
0
引用数:
0
h-index:
0
机构:
NINCDS,DEV & METAB NEUROL BRANCH,BETHESDA,MD 20014
PENTCHEV, PG
FURBISH, FS
论文数:
0
引用数:
0
h-index:
0
机构:
NINCDS,DEV & METAB NEUROL BRANCH,BETHESDA,MD 20014
FURBISH, FS
SUZUKI, K
论文数:
0
引用数:
0
h-index:
0
机构:
NINCDS,DEV & METAB NEUROL BRANCH,BETHESDA,MD 20014
SUZUKI, K
TANAKA, H
论文数:
0
引用数:
0
h-index:
0
机构:
NINCDS,DEV & METAB NEUROL BRANCH,BETHESDA,MD 20014
TANAKA, H
SCHNEIDER, EL
论文数:
0
引用数:
0
h-index:
0
机构:
NINCDS,DEV & METAB NEUROL BRANCH,BETHESDA,MD 20014
SCHNEIDER, EL
[J].
CLINICA CHIMICA ACTA,
1977,
77
(01)
: 53
-
59
[6]
SPECTROPHOTOMETRIC METHOD FOR DETERMINATION OF SPHINGOMYELINASE
GATT, S
论文数:
0
引用数:
0
h-index:
0
GATT, S
DINUR, T
论文数:
0
引用数:
0
h-index:
0
DINUR, T
BARENHOLZ, Y
论文数:
0
引用数:
0
h-index:
0
BARENHOLZ, Y
[J].
BIOCHIMICA ET BIOPHYSICA ACTA,
1978,
530
(03)
: 503
-
507
[7]
GATT S, 1980, CLIN CHEM, V26, P93
[8]
SYNTHESIS OF TRINITROPHENYLAMINOLAURIC ACID AND USE OF ITS GLYCERYL ESTERS FOR ASSAYING LIPASE BY A SPECTROPHOTOMETRIC PROCEDURE
GOLDBERG, R
论文数:
0
引用数:
0
h-index:
0
机构:
HEBREW UNIV JERUSALEM,HADASSAH MED SCH,DEPT BIOCHEM,NEUROCHEM LAB,JERUSALEM 91000,ISRAEL
HEBREW UNIV JERUSALEM,HADASSAH MED SCH,DEPT BIOCHEM,NEUROCHEM LAB,JERUSALEM 91000,ISRAEL
GOLDBERG, R
BARENHOLZ, Y
论文数:
0
引用数:
0
h-index:
0
机构:
HEBREW UNIV JERUSALEM,HADASSAH MED SCH,DEPT BIOCHEM,NEUROCHEM LAB,JERUSALEM 91000,ISRAEL
HEBREW UNIV JERUSALEM,HADASSAH MED SCH,DEPT BIOCHEM,NEUROCHEM LAB,JERUSALEM 91000,ISRAEL
BARENHOLZ, Y
GATT, S
论文数:
0
引用数:
0
h-index:
0
机构:
HEBREW UNIV JERUSALEM,HADASSAH MED SCH,DEPT BIOCHEM,NEUROCHEM LAB,JERUSALEM 91000,ISRAEL
HEBREW UNIV JERUSALEM,HADASSAH MED SCH,DEPT BIOCHEM,NEUROCHEM LAB,JERUSALEM 91000,ISRAEL
GATT, S
[J].
BIOCHIMICA ET BIOPHYSICA ACTA,
1978,
531
(02)
: 237
-
241
[9]
HAMMARSTROM S, 1971, J LIPID RES, V12, P760
[10]
LOWRY OH, 1951, J BIOL CHEM, V193, P265
←
1
2
→