GAUCHER DISEASE - ISOLATION AND COMPARISON OF NORMAL AND MUTANT GLUCOCEREBROSIDASE FROM HUMAN SPLEEN TISSUE

被引：47

作者：

PENTCHEV, PG ^{[1
]}

BRADY, RO ^{[1
]}

BLAIR, HE ^{[1
]}

BRITTON, DE ^{[1
]}

SORRELL, SH ^{[1
]}

机构：

[1] TUFTS UNIV,SCH MED,NEW ENGLAND ENZYME CTR,BOSTON,MA 02111

来源：

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA | 1978年 / 75卷 / 08期

关键词：

D O I：

10.1073/pnas.75.8.3970

中图分类号：

O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];

学科分类号：

07 ; 0710 ; 09 ;

摘要：

引用

页码：3970 / 3973

页数：4

共 14 条

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[4] AUTOLYSIS OF GLYCOPROTEINS IN RAT-KIDNEY LYSOSOMES INVITRO - EFFECTS ON ISOELECTRIC FOCUSING BEHAVIOR OF GLYCOPROTEINS, ARYLSULFATASE AND BETA-GLUCURONIDASE [J].

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[5] GAUCHERS DISEASE - DEFICIENCY OF ACID BETA-GLUCOSIDASE AND RECONSTITUTION OF ENZYME ACTIVITY IN-VITRO [J].

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[6]

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LOWRY OH, 1951, J BIOL CHEM, V193, P265

[10]

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