LIVER-TRANSPLANTATION FOR PROTOPORPHYRIA - EVIDENCE FOR THE PREDOMINANT ROLE OF THE ERYTHROPOIETIC TISSUE IN PROTOPORPHYRIN OVERPRODUCTION

被引:61
作者
SAMUEL, D
BOBOC, B
BERNUAU, J
BISMUTH, H
BENHAMOU, JP
机构
[1] HOP BEAUJON,INSERM,UNITE RECH PHYSIOPATHOL HEPAT,F-92118 CLICHY,FRANCE
[2] HOP PAUL BROUSSE,SERV CHIRURGIE HEPATOBILIAIRE,F-94800 VILLEJUIF,FRANCE
关键词
D O I
10.1016/S0016-5085(88)80033-7
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
引用
收藏
页码:816 / 819
页数:4
相关论文
共 11 条
[1]   TRANSFUSION THERAPY IN A PATIENT WITH ERYTHROPOIETIC PROTOPORPHYRIA [J].
BECHTEL, MA ;
BERTOLONE, SJ ;
HODGE, SJ .
ARCHIVES OF DERMATOLOGY, 1981, 117 (02) :99-101
[2]  
Bloomer J R, 1982, Semin Liver Dis, V2, P143, DOI 10.1055/s-2008-1040704
[3]   EFFECT OF HEMATIN ADMINISTRATION TO PATIENTS WITH PROTOPORPHYRIA AND LIVER-DISEASE [J].
BLOOMER, JR ;
PIERACH, CA .
HEPATOLOGY, 1982, 2 (06) :817-821
[4]  
BONKOWSKY HL, 1966, GASTROENTEROLOGY, V90, P191
[5]   THE INHERITED ENZYMATIC DEFECT IN PORPHYRIA VARIEGATA [J].
DEYBACH, JC ;
DEVERNEUIL, H ;
NORDMANN, Y .
HUMAN GENETICS, 1981, 58 (04) :425-428
[6]   IRON THERAPY FOR HEPATIC-DYSFUNCTION IN ERYTHROPOIETIC PROTOPORPHYRIA [J].
GORDEUK, VR ;
BRITTENHAM, GM ;
HAWKINS, CW ;
MUKHTAR, H ;
BICKERS, DR .
ANNALS OF INTERNAL MEDICINE, 1986, 105 (01) :27-31
[7]  
PIMSTONE NR, 1986, HEPATOLOGY, V6, P1176
[8]   PROTOPORPHYRIN HEPATOPATHY - EFFECTS OF CHOLIC-ACID INGESTION IN MURINE GRISEOFULVIN-INDUCED PROTOPORPHYRIA [J].
POHFITZPATRICK, MB ;
SKLAR, JA ;
GOLDSMAN, C ;
LEFKOWITCH, JH .
JOURNAL OF CLINICAL INVESTIGATION, 1983, 72 (04) :1449-1458
[9]   CHANGES IN PROTOPORPHYRIN DISTRIBUTION DYNAMICS DURING LIVER-FAILURE AND RECOVERY IN A PATIENT WITH PROTOPORPHYRIA AND EPSTEIN-BARR VIRAL-HEPATITIS [J].
POHFITZPATRICK, MB ;
WHITLOCK, RT ;
LEFTKOWITCH, JH .
AMERICAN JOURNAL OF MEDICINE, 1986, 80 (05) :943-950
[10]  
SCHWARTZ SAMUEL, 1960, METHODS BIOCHEM ANAL, V8, P221