AUTONOMIC FUNCTION;
HEREDITARY MOTOR AND SENSORY NEUROPATHY;
CHARCOT-MARIE-TOOTH DISEASE;
CARDIOVASCULAR REFLEXES;
SWEAT TEST;
D O I:
10.1002/mus.880141107
中图分类号:
R74 [神经病学与精神病学];
学科分类号:
摘要:
Autonomic tests of heart rate and blood pressure control using both invasive and noninvasive techniques were performed on 11 patients with hereditary motor and sensory neuropathy (HMSN) types 1, and 4 patients with HMSN type 2. The results were compared with those of 76 control subjects. No significant difference was found between the patient and control groups. Impairment of sweating on the extremities was found in patients with HMSN types 1 and 2, consistent with distal degeneration of sympathetic fibers in peripheral nerves, but there were no abnormalities of cardiovascular reflex control mechanisms.