ROLE OF LYSOSOMES IN PATHOGENICITY OF STORAGE DISEASES

被引:9
作者
HERS, HG
机构
关键词
D O I
10.1016/S0300-9084(72)80179-2
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 [生物化学与分子生物学]; 081704 [应用化学];
摘要
引用
收藏
页码:753 / &
相关论文
共 17 条
[1]
METACHROMATIC FORM OF DIFFUSE CEREBRAL SCLEROSIS .V. NATURE AND SIGNIFICANCE OF LOW SULFATASE ACTIVITY - A CONTROLLED STUDY OF BRAIN LIVER AND KIDNEY IN 4 PATIENTS WITH METACHROMATIC LEUKODYSTROPHY (MLD) [J].
AUSTIN, J ;
ARMSTRONG, D ;
SHEARER, L .
ARCHIVES OF NEUROLOGY, 1965, 13 (06) :593-+
[2]
BAUDHUIN P, 1964, LAB INVEST, V13, P1139
[3]
METABOLISM OF GLUCOCEREBROSIDES .2. EVIDENCE OF AN ENZYMATIC DEFICIENCY IN GAUCHERS DISEASE [J].
BRADY, RO ;
KANFER, JN ;
SHAPIRO, D .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1965, 18 (02) :221-&
[4]
METABOLISM OF SPHINGOMYELIN .2. EVIDENCE OF AN ENZYMATIC DEFICIENCY IN NIEMANN-PICK DISEASE [J].
BRADY, RO ;
KANFER, JN ;
MOCK, MB ;
FREDRICKSON, DS .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1966, 55 (02) :366-+
[5]
GM1-GANGLIOSIDE ACCUMULATION AND BETA-GALACTOSIDASE DEFICIENCY IN A CASE OF GM1-GANGLIOSIDOSIS (LANDING DISEASE) [J].
DACREMONT, G ;
KINT, JA .
CLINICA CHIMICA ACTA, 1968, 21 (03) :421-+
[6]
FUNCTIONS OF LYSOSOMES [J].
DEDUVE, C ;
WATTIAUX, R .
ANNUAL REVIEW OF PHYSIOLOGY, 1966, 28 :435-+
[7]
HERS HG, 1965, GASTROENTEROLOGY, V48, P625
[9]
ILLINGWORTH B, 1956, J BIOL CHEM, V218, P123
[10]
KINT J A, 1970, Science (Washington D C), V167, P1268, DOI 10.1126/science.167.3922.1268