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A NEW VARIANT OF TYPE-IV GLYCOGENOSIS - DEFICIENCY OF BRANCHING ENZYME-ACTIVITY WITHOUT APPARENT PROGRESSIVE LIVER-DISEASE
被引:49
作者
:
GREENE, HL
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV,SCH MED,DEPT BIOCHEM,ST LOUIS,MO 63110
GREENE, HL
BROWN, BI
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV,SCH MED,DEPT BIOCHEM,ST LOUIS,MO 63110
BROWN, BI
MCCLENATHAN, DT
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV,SCH MED,DEPT BIOCHEM,ST LOUIS,MO 63110
MCCLENATHAN, DT
AGOSTINI, RM
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV,SCH MED,DEPT BIOCHEM,ST LOUIS,MO 63110
AGOSTINI, RM
TAYLOR, SR
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV,SCH MED,DEPT BIOCHEM,ST LOUIS,MO 63110
TAYLOR, SR
机构
:
[1]
WASHINGTON UNIV,SCH MED,DEPT BIOCHEM,ST LOUIS,MO 63110
[2]
CHILDRENS HOSP,DEPT PATHOL,PITTSBURGH,PA 15213
[3]
ALL CHILDRENS HOSP,DEPT GASTROENTEROL,ST PETERSBURG,FL 33701
来源
:
HEPATOLOGY
|
1988年
/ 8卷
/ 02期
关键词
:
D O I
:
10.1002/hep.1840080219
中图分类号
:
R57 [消化系及腹部疾病];
学科分类号
:
摘要
:
引用
收藏
页码:302 / 306
页数:5
相关论文
共 18 条
[1]
ANDERSEN DH, 1956, LAB INVEST, V5, P11
[2]
BANNAYAN GA, 1976, AM J CLIN PATHOL, V66, P702
[3]
LACK OF AN ALPHA-1,4-GLUCAN - ALPHA-1,4-GLUCAN 6-GLYCOSYL TRANSFERASE IN A CASE OF TYPE 4 GLYCOGENOSIS
BROWN, BI
论文数:
0
引用数:
0
h-index:
0
BROWN, BI
BROWN, DH
论文数:
0
引用数:
0
h-index:
0
BROWN, DH
[J].
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA,
1966,
56
(02)
: 725
-
&
[4]
BROWN BI, 1985, CONGENITAL METABOLIC, P227
[5]
BROWN DH, 1978, J BIOL CHEM, V253, P5005
[6]
STUDIES OF THE RESIDUAL GLYCOGEN BRANCHING ENZYME-ACTIVITY PRESENT IN HUMAN-SKIN FIBROBLASTS FROM PATIENTS WITH TYPE-IV GLYCOGEN-STORAGE DISEASE
BROWN, DH
论文数:
0
引用数:
0
h-index:
0
BROWN, DH
BROWN, BI
论文数:
0
引用数:
0
h-index:
0
BROWN, BI
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1983,
111
(02)
: 636
-
643
[7]
AN ADULT CASE OF ANDERSENS DISEASE - TYPE-IV GLYCOGENOSIS - A CLINICAL, HISTOCHEMICAL, ULTRASTRUCTURAL AND BIOCHEMICAL-STUDY
FERGUSON, IT
论文数:
0
引用数:
0
h-index:
0
机构:
WITHINGTON HOSP,DEPT NEUROL,MANCHESTER M20 8LR,LANCS,ENGLAND
FERGUSON, IT
MAHON, M
论文数:
0
引用数:
0
h-index:
0
机构:
WITHINGTON HOSP,DEPT NEUROL,MANCHESTER M20 8LR,LANCS,ENGLAND
MAHON, M
CUMMING, WJK
论文数:
0
引用数:
0
h-index:
0
机构:
WITHINGTON HOSP,DEPT NEUROL,MANCHESTER M20 8LR,LANCS,ENGLAND
CUMMING, WJK
[J].
JOURNAL OF THE NEUROLOGICAL SCIENCES,
1983,
60
(03)
: 337
-
351
[8]
CARDIOMYOPATHY CIRRHOSIS OF LIVER AND DEPOSITS OF A FIBRILLAR POLYSACCHARIDE - REPORT OF A CASE WITH HISTOCHEMICAL AND ELECTRON MICROSCOPIC STUDIES
FERRANS, VJ
论文数:
0
引用数:
0
h-index:
0
FERRANS, VJ
HIBBS, RG
论文数:
0
引用数:
0
h-index:
0
HIBBS, RG
WALSH, JJ
论文数:
0
引用数:
0
h-index:
0
WALSH, JJ
BURCH, GE
论文数:
0
引用数:
0
h-index:
0
BURCH, GE
[J].
AMERICAN JOURNAL OF CARDIOLOGY,
1966,
17
(04)
: 457
-
+
[9]
GREENE GM, 1987, ARCH PATHOL LAB MED, V111, P977
[10]
HYPOGLYCEMIA IN TYPE-IV GLYCOGENOSIS - HEPATIC IMPROVEMENT IN 2 PATIENTS WITH NUTRITIONAL MANAGEMENT
GREENE, HL
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT BIOCHEM, ST LOUIS, MO 63110 USA
GREENE, HL
GHISHAN, FK
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT BIOCHEM, ST LOUIS, MO 63110 USA
GHISHAN, FK
BROWN, B
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT BIOCHEM, ST LOUIS, MO 63110 USA
BROWN, B
MCCLENATHAN, DT
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT BIOCHEM, ST LOUIS, MO 63110 USA
MCCLENATHAN, DT
FREESE, D
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT BIOCHEM, ST LOUIS, MO 63110 USA
FREESE, D
[J].
JOURNAL OF PEDIATRICS,
1988,
112
(01)
: 55
-
58
←
1
2
→
共 18 条
[1]
ANDERSEN DH, 1956, LAB INVEST, V5, P11
[2]
BANNAYAN GA, 1976, AM J CLIN PATHOL, V66, P702
[3]
LACK OF AN ALPHA-1,4-GLUCAN - ALPHA-1,4-GLUCAN 6-GLYCOSYL TRANSFERASE IN A CASE OF TYPE 4 GLYCOGENOSIS
BROWN, BI
论文数:
0
引用数:
0
h-index:
0
BROWN, BI
BROWN, DH
论文数:
0
引用数:
0
h-index:
0
BROWN, DH
[J].
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA,
1966,
56
(02)
: 725
-
&
[4]
BROWN BI, 1985, CONGENITAL METABOLIC, P227
[5]
BROWN DH, 1978, J BIOL CHEM, V253, P5005
[6]
STUDIES OF THE RESIDUAL GLYCOGEN BRANCHING ENZYME-ACTIVITY PRESENT IN HUMAN-SKIN FIBROBLASTS FROM PATIENTS WITH TYPE-IV GLYCOGEN-STORAGE DISEASE
BROWN, DH
论文数:
0
引用数:
0
h-index:
0
BROWN, DH
BROWN, BI
论文数:
0
引用数:
0
h-index:
0
BROWN, BI
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1983,
111
(02)
: 636
-
643
[7]
AN ADULT CASE OF ANDERSENS DISEASE - TYPE-IV GLYCOGENOSIS - A CLINICAL, HISTOCHEMICAL, ULTRASTRUCTURAL AND BIOCHEMICAL-STUDY
FERGUSON, IT
论文数:
0
引用数:
0
h-index:
0
机构:
WITHINGTON HOSP,DEPT NEUROL,MANCHESTER M20 8LR,LANCS,ENGLAND
FERGUSON, IT
MAHON, M
论文数:
0
引用数:
0
h-index:
0
机构:
WITHINGTON HOSP,DEPT NEUROL,MANCHESTER M20 8LR,LANCS,ENGLAND
MAHON, M
CUMMING, WJK
论文数:
0
引用数:
0
h-index:
0
机构:
WITHINGTON HOSP,DEPT NEUROL,MANCHESTER M20 8LR,LANCS,ENGLAND
CUMMING, WJK
[J].
JOURNAL OF THE NEUROLOGICAL SCIENCES,
1983,
60
(03)
: 337
-
351
[8]
CARDIOMYOPATHY CIRRHOSIS OF LIVER AND DEPOSITS OF A FIBRILLAR POLYSACCHARIDE - REPORT OF A CASE WITH HISTOCHEMICAL AND ELECTRON MICROSCOPIC STUDIES
FERRANS, VJ
论文数:
0
引用数:
0
h-index:
0
FERRANS, VJ
HIBBS, RG
论文数:
0
引用数:
0
h-index:
0
HIBBS, RG
WALSH, JJ
论文数:
0
引用数:
0
h-index:
0
WALSH, JJ
BURCH, GE
论文数:
0
引用数:
0
h-index:
0
BURCH, GE
[J].
AMERICAN JOURNAL OF CARDIOLOGY,
1966,
17
(04)
: 457
-
+
[9]
GREENE GM, 1987, ARCH PATHOL LAB MED, V111, P977
[10]
HYPOGLYCEMIA IN TYPE-IV GLYCOGENOSIS - HEPATIC IMPROVEMENT IN 2 PATIENTS WITH NUTRITIONAL MANAGEMENT
GREENE, HL
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT BIOCHEM, ST LOUIS, MO 63110 USA
GREENE, HL
GHISHAN, FK
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT BIOCHEM, ST LOUIS, MO 63110 USA
GHISHAN, FK
BROWN, B
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT BIOCHEM, ST LOUIS, MO 63110 USA
BROWN, B
MCCLENATHAN, DT
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT BIOCHEM, ST LOUIS, MO 63110 USA
MCCLENATHAN, DT
FREESE, D
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT BIOCHEM, ST LOUIS, MO 63110 USA
FREESE, D
[J].
JOURNAL OF PEDIATRICS,
1988,
112
(01)
: 55
-
58
←
1
2
→