A NEW VARIANT OF TYPE-IV GLYCOGENOSIS - DEFICIENCY OF BRANCHING ENZYME-ACTIVITY WITHOUT APPARENT PROGRESSIVE LIVER-DISEASE

被引:49
作者
GREENE, HL
BROWN, BI
MCCLENATHAN, DT
AGOSTINI, RM
TAYLOR, SR
机构
[1] WASHINGTON UNIV,SCH MED,DEPT BIOCHEM,ST LOUIS,MO 63110
[2] CHILDRENS HOSP,DEPT PATHOL,PITTSBURGH,PA 15213
[3] ALL CHILDRENS HOSP,DEPT GASTROENTEROL,ST PETERSBURG,FL 33701
关键词
D O I
10.1002/hep.1840080219
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
引用
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页码:302 / 306
页数:5
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