ENHANCED DEGRADATION OF TRYPSIN-TREATED LOW-DENSITY LIPOPROTEIN BY FIBROBLASTS FROM A PATIENT WITH HOMOZYGOUS FAMILIAL HYPERCHOLESTEROLEMIA

被引:21
作者
CAREW, TE [1 ]
CHAPMAN, MJ [1 ]
GOLDSTEIN, S [1 ]
STEINBERG, D [1 ]
机构
[1] INST NATL SANTE & RECH MED,UNITE RECH METAB LIPIDES,UNITE 35,F-94010 CRETEIL,FRANCE
关键词
D O I
10.1016/0005-2760(78)90115-7
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:171 / 175
页数:5
相关论文
共 12 条
  • [1] ANALYSIS OF A MUTANT STRAIN OF HUMAN FIBROBLASTS WITH A DEFECT IN INTERNALIZATION OF RECEPTOR-BOUND LOW-DENSITY LIPOPROTEIN
    BROWN, MS
    GOLDSTEIN, JL
    [J]. CELL, 1976, 9 (04) : 663 - 674
  • [2] RECEPTOR-MEDIATED CONTROL OF CHOLESTEROL-METABOLISM
    BROWN, MS
    GOLDSTEIN, JL
    [J]. SCIENCE, 1976, 191 (4223) : 150 - 154
  • [3] REGULATION OF ACTIVITY OF LOW-DENSITY LIPOPROTEIN RECEPTOR IN HUMAN FIBROBLASTS
    BROWN, MS
    GOLDSTEIN, JL
    [J]. CELL, 1975, 6 (03) : 307 - 316
  • [4] CHAPMAN MJ, 1976, ATHEROSCLEROSIS, V25, P267
  • [5] CHAPMAN MJ, 1976, 19TH P INT C BIOCH L, P12
  • [6] ALTERATIONS IN CELL-SURFACE GLYCOSPHINGOLIPIDS AND OTHER LIPID CLASSES OF FIBROBLASTS IN FAMILIAL HYPERCHOLESTEROLEMIA
    CHATTERJEE, S
    SEKERKE, CS
    KWITEROVICH, PO
    [J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1976, 73 (12) : 4339 - 4343
  • [7] PLAQUE PRODUCTION BY THE POLYOMA VIRUS
    DULBECCO, R
    FREEMAN, G
    [J]. VIROLOGY, 1959, 8 (03) : 396 - 397
  • [8] FOGELMAN AM, 1977, J BIOL CHEM, V252, P644
  • [9] INTERACTION BETWEEN HIGH-DENSITY AND LOW-DENSITY LIPOPROTEINS DURING UPTAKE AND DEGRADATION BY CULTURED HUMAN FIBROBLASTS
    MILLER, NE
    WEINSTEIN, DB
    CAREW, TE
    KOSCHINSKY, T
    STEINBERG, D
    [J]. JOURNAL OF CLINICAL INVESTIGATION, 1977, 60 (01) : 78 - 88
  • [10] MILLER NE, J LIPID RES