NEW PHENOTYPIC VARIANT OF ADRENOLEUKODYSTROPHY - PATHOLOGIC, ULTRASTRUCTURAL, AND BIOCHEMICAL-STUDY IN 2 BROTHERS

被引:60
作者
MANZ, HJ
SCHUELEIN, M
MCCULLOUGH, DC
KISHIMOTO, Y
EIBEN, RM
机构
[1] GEORGETOWN UNIV,MED CTR,DEPT PEDIAT & NEUROL,WASHINGTON,DC 20007
[2] GEORGETOWN UNIV,MED CTR,DEPT SURG & NEUROSURG,WASHINGTON,DC 20007
[3] CLEVELAND METROPOLITAN GEN HOSP,DEPT PEDIAT,CLEVELAND,OH 44109
[4] CLEVELAND METROPOLITAN GEN HOSP,DEPT NEUROL,CLEVELAND,OH 44109
[5] JOHNS HOPKINS UNIV HOSP,SCH MED,JOHN F KENNEDY INST,BALTIMORE,MD 21205
[6] JOHNS HOPKINS UNIV HOSP,SCH MED,DEPT NEUROL,BALTIMORE,MD 21205
关键词
D O I
10.1016/0022-510X(80)90169-0
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:245 / 260
页数:16
相关论文
共 20 条
  • [11] JOHANNESSEN JVI, 1977, PATHOLOGY ANNUAL 2, V12
  • [12] PATHOLOGY AND PATHOGENESIS OF VIRAL-INFECTIONS OF CENTRAL NERVOUS-SYSTEM
    MANZ, HJ
    [J]. HUMAN PATHOLOGY, 1977, 8 (01) : 3 - 26
  • [13] ADRENOLEUKODYSTROPHY - ACCUMULATION OF CHOLESTEROL ESTERS WITH VERY LONG-CHAIN FATTY-ACIDS
    MENKES, JH
    CORBO, LM
    [J]. NEUROLOGY, 1977, 27 (10) : 928 - 932
  • [14] ADRENOLEUKODYSTROPHY - ELECTRON-MICROSCOPIC FINDINGS
    POWELL, H
    TINDALL, R
    SCHULTZ, P
    PAA, D
    OBRIEN, J
    LAMPERT, P
    [J]. ARCHIVES OF NEUROLOGY, 1975, 32 (04) : 250 - 260
  • [15] ADRENO-LEUKODYSTROPHY - SIMILAR ULTRASTRUCTURAL CHANGES IN ADRENAL CORTICAL AND SCHWANN-CELLS
    POWERS, JM
    SCHAUMBU.HH
    [J]. ARCHIVES OF NEUROLOGY, 1974, 30 (05) : 406 - 408
  • [16] POWERS JM, 1974, AM J PATHOL, V76, P481
  • [17] COMPUTERIZED TOMOGRAPHY IN DEMYELINATING DISEASE OF YOUNG
    ROBERTSON, WC
    GOMEZ, MR
    REESE, DF
    OKAZAKI, H
    [J]. NEUROLOGY, 1977, 27 (09) : 838 - 842
  • [18] ADRENOLEUKODYSTROPHY - CLINICAL AND PATHOLOGICAL-STUDY OF 17 CASES
    SCHAUMBURG, HH
    POWERS, JM
    RAINE, CS
    SUZUKI, K
    RICHARDSON, EP
    [J]. ARCHIVES OF NEUROLOGY, 1975, 32 (09) : 577 - 591
  • [19] ADRENOMYELONEUROPATHY - PROBABLE VARIANT OF ADRENOLEUKODYSTROPHY .2. GENERAL PATHOLOGIC, NEUROPATHOLOGIC, AND BIOCHEMICAL ASPECTS
    SCHAUMBURG, HH
    POWERS, JM
    RAINE, CS
    SPENCER, PS
    GRIFFIN, JW
    PRINEAS, JW
    BOEHME, DM
    [J]. NEUROLOGY, 1977, 27 (12) : 1114 - 1119
  • [20] ULRICH J, 1978, ACTA NEUROPATHOL, V43, P77