MITOCHONDRIAL MYOPATHY, ENCEPHALOPATHY, LACTIC-ACIDOSIS, AND STROKELIKE EPISODES WITH RECURRENT ABDOMINAL SYMPTOMS AND COENZYME-Q10 ADMINISTRATION

被引:58
作者
YAMAMOTO, M
SATO, T
ANNO, M
UJIKE, H
TAKEMOTO, M
机构
[1] SUMITOMO BESHI HOSP,DEPT NEUROSURG,NIIHAMA,JAPAN
[2] JUNTENDO UNIV,SCH MED,DEPT NEUROL,TOKYO 113,JAPAN
关键词
D O I
10.1136/jnnp.50.11.1475
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:1475 / 1481
页数:7
相关论文
共 20 条
[11]   MITOCHONDRIAL MYOPATHY CHARACTERIZED BY A DEFICIENCY IN REDUCIBLE CYTOCHROME-B [J].
MORGANHUGHES, JA ;
DARVENIZA, P ;
KAHN, SN ;
LANDON, DN ;
SHERRATT, RM ;
LAND, JM ;
CLARK, JB .
BRAIN, 1977, 100 (DEC) :617-640
[12]  
MULLERHOCKER J, 1983, VIRCHOWS ARCH A, V399, P11
[13]   TREATMENT OF KEARNS-SAYRE SYNDROME WITH COENZYME-Q10 [J].
OGASAHARA, S ;
NISHIKAWA, Y ;
YORIFUJI, S ;
SOGA, F ;
NAKAMURA, Y ;
TAKAHASHI, M ;
HASHIMOTO, S ;
KONO, N ;
TARUI, S .
NEUROLOGY, 1986, 36 (01) :45-53
[14]   IMPROVEMENT OF ABNORMAL PYRUVATE METABOLISM AND CARDIAC CONDUCTION DEFECT WITH COENZYME-Q10 IN KEARNS-SAYRE SYNDROME [J].
OGASAHARA, S ;
YORIFUJI, S ;
NISHIKAWA, Y ;
TAKAHASHI, M ;
WADA, K ;
HAZAMA, T ;
NAKAMURA, Y ;
HASHIMOTO, S ;
KONO, N ;
TARUI, S .
NEUROLOGY, 1985, 35 (03) :372-377
[15]   MITOCHONDRIAL MYOPATHY, ENCEPHALOPATHY, LACTIC-ACIDOSIS, AND STROKELIKE EPISODES - A DISTINCTIVE CLINICAL SYNDROME [J].
PAVLAKIS, SG ;
PHILLIPS, PC ;
DIMAURO, S ;
DEVIVO, DC ;
ROWLAND, LP .
ANNALS OF NEUROLOGY, 1984, 16 (04) :481-488
[16]  
SEKUZU I, 1960, J BIOCHEM-TOKYO, V48, P214
[17]   NONDROPLET ULTRASTRUCTURAL DEMONSTRATION OF CYTOCHROME OXIDASE ACTIVITY WITH A POLYMERIZING OSMIOPHILIC REAGENT DIAMINOBENZIDINE (DAB) [J].
SELIGMAN, AM ;
KARNOVSKY, MJ ;
WASSERKRUG, HL ;
HANKER, JS .
JOURNAL OF CELL BIOLOGY, 1968, 38 (01) :1-+
[18]  
SHAPIRA Y, 1977, ISRAEL J MED SCI, V13, P161
[19]   MITOCHONDRIAL ENCEPHALOMYOPATHY - FLUCTUATING SYMPTOMS AND CT [J].
YAMAMOTO, T ;
BEPPU, H ;
TSUBAKI, T .
NEUROLOGY, 1984, 34 (11) :1456-1460
[20]  
ZIEGLER D, 1967, METHOD ENZYMOL, V10, P231