THE SCID DEFECT AFFECTS THE FINAL STEP OF THE IMMUNOGLOBULIN VDJ RECOMBINASE MECHANISM

被引:285
作者
MALYNN, BA
BLACKWELL, TK
FULOP, GM
RATHBUN, GA
FURLEY, AJW
FERRIER, P
HEINKE, LB
PHILLIPS, RA
YANCOPOULOS, GD
ALT, FW
机构
[1] COLUMBIA UNIV COLL PHYS & SURG,DEPT BIOCHEM,NEW YORK,NY 10032
[2] COLUMBIA UNIV COLL PHYS & SURG,DEPT MICROBIOL,NEW YORK,NY 10032
[3] UNIV TORONTO,DEPT MED GENET,TORONTO M5S 1A1,ONTARIO,CANADA
[4] HOSP SICK CHILDREN,DIV HAEMATOL ONCOL,TORONTO M5G 1X8,ONTARIO,CANADA
关键词
D O I
10.1016/0092-8674(88)90066-9
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:453 / 460
页数:8
相关论文
共 48 条
  • [1] ORGANIZATION AND REORGANIZATION OF IMMUNOGLOBULIN GENES IN A-MULV TRANSFORMED-CELLS - REARRANGEMENT OF HEAVY BUT NOT LIGHT CHAIN GENES
    ALT, F
    ROSENBERG, N
    LEWIS, S
    THOMAS, E
    BALTIMORE, D
    [J]. CELL, 1981, 27 (02) : 381 - 390
  • [2] IMMUNOGLOBULIN HEAVY-CHAIN EXPRESSION AND CLASS SWITCHING IN A MURINE LEUKEMIA-CELL LINE
    ALT, FW
    ROSENBERG, N
    CASANOVA, RJ
    THOMAS, E
    BALTIMORE, D
    [J]. NATURE, 1982, 296 (5855) : 325 - 331
  • [3] ORDERED REARRANGEMENT OF IMMUNOGLOBULIN HEAVY-CHAIN VARIABLE REGION SEGMENTS
    ALT, FW
    YANCOPOULOS, GD
    BLACKWELL, TK
    WOOD, C
    THOMAS, E
    BOSS, M
    COFFMAN, R
    ROSENBERG, N
    TONEGAWA, S
    BALTIMORE, D
    [J]. EMBO JOURNAL, 1984, 3 (06) : 1209 - 1219
  • [4] REGULATION OF GENOME REARRANGEMENT EVENTS DURING LYMPHOCYTE DIFFERENTIATION
    ALT, FW
    BLACKWELL, TK
    DEPINHO, RA
    RETH, MG
    YANCOPOULOS, GD
    [J]. IMMUNOLOGICAL REVIEWS, 1986, 89 : 5 - 30
  • [5] JOINING OF IMMUNOGLOBULIN HEAVY-CHAIN GENE SEGMENTS - IMPLICATIONS FROM A CHROMOSOME WITH EVIDENCE OF 3 D-JH FUSIONS
    ALT, FW
    BALTIMORE, D
    [J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1982, 79 (13): : 4118 - 4122
  • [6] DEVELOPMENT OF THE PRIMARY ANTIBODY REPERTOIRE
    ALT, FW
    BLACKWELL, TK
    YANCOPOULOS, GD
    [J]. SCIENCE, 1987, 238 (4830) : 1079 - 1087
  • [7] ALT FW, 1982, CELL BIOL, V2, P386
  • [8] MECHANISM OF THE T(14-18) CHROMOSOMAL TRANSLOCATION - STRUCTURAL-ANALYSIS OF BOTH DERIVATIVE-14 AND DERIVATIVE-18 RECIPROCAL PARTNERS
    BAKHSHI, A
    WRIGHT, JJ
    GRANINGER, W
    SETO, M
    OWENS, J
    COSSMAN, J
    JENSEN, JP
    GOLDMAN, P
    KORSMEYER, SJ
    [J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1987, 84 (08) : 2396 - 2400
  • [9] IMMUNOGLOBULIN VH REGION GENES OF THE MOUSE ARE ORGANIZED IN OVERLAPPING CLUSTERS
    BLANKENSTEIN, T
    KRAWINKEL, U
    [J]. EUROPEAN JOURNAL OF IMMUNOLOGY, 1987, 17 (09) : 1351 - 1357
  • [10] A SEVERE COMBINED IMMUNODEFICIENCY MUTATION IN THE MOUSE
    BOSMA, GC
    CUSTER, RP
    BOSMA, MJ
    [J]. NATURE, 1983, 301 (5900) : 527 - 530