DIETARY ERUCIC-ACID THERAPY FOR X-LINKED ADRENOLEUKODYSTROPHY

被引：164

作者：

RIZZO, WB

LESHNER, RT

ODONE, A

DAMMANN, AL

CRAFT, DA

JENSEN, ME

JENNINGS, SS

DAVIS, S

JAITLY, R

SGRO, JA

机构：

[1] VIRGINIA COMMONWEALTH UNIV,MED COLL VIRGINIA,DEPT HUMAN GENET,RICHMOND,VA 23298

[2] VIRGINIA COMMONWEALTH UNIV,MED COLL VIRGINIA,DEPT NEUROL,RICHMOND,VA 23298

[3] VIRGINIA COMMONWEALTH UNIV,MED COLL VIRGINIA,DEPT RADIOL,RICHMOND,VA 23298

[4] VIRGINIA COMMONWEALTH UNIV,MED COLL VIRGINIA,DEPT MED,RICHMOND,VA 23298

[5] UNIV CALIF DAVIS,DEPT NEUROL,DAVIS,CA 95616

来源：

NEUROLOGY | 1989年 / 39卷 / 11期

关键词：

D O I：

10.1212/WNL.39.11.1415

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

引用

页码：1415 / 1422

页数：8

共 28 条

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[5] ADRENOLEUKODYSTROPHY - THE CHAIN SHORTENING OF ERUCIC-ACID (22-1(N-9)) AND ADRENIC ACID (22-4(N-6)) IS DEFICIENT IN NEONATAL ADRENOLEUKODYSTROPHY AND NORMAL IN X-LINKED ADRENOLEUKODISTROPHY SKIN FIBROBLASTS
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[9] ACTH RECEPTOR DEFECT IN ADRENOLEUKODYSTROPHY (ALD)
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[10] A NEW DIETARY THERAPY FOR ADRENOLEUKODYSTROPHY - BIOCHEMICAL AND PRELIMINARY CLINICAL-RESULTS IN 36 PATIENTS
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