HEREDITARY AND NON-HEREDITARY FORM OF CHRONIC HEPATIC PORPHYRIA - DIFFERENT BEHAVIOR OF UROPORPHYRINOGEN DECARBOXYLASE IN LIVER AND ERYTHROCYTES

被引:29
作者
DOSS, M
VONTIEPERMANN, R
LOOK, D
HENNING, H
NIKOLOWSKI, J
RYCKMANNS, F
BRAUNFALCO, O
机构
[1] UNIV MUNICH, DERMATOL KLIN & POLIKLIN, D-8000 MUNICH 22, FED REP GER
[2] BFA, FOHRENKAMP KLIN, MOLLN, FED REP GER
来源
KLINISCHE WOCHENSCHRIFT | 1980年 / 58卷 / 24期
关键词
D O I
10.1007/BF01477732
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:1347 / 1356
页数:10
相关论文
共 43 条
[21]  
GOERZ G, 1979, FORTSCHR MED, V97, P1548
[22]   PORPHYRIA CUTANEA-TARDA - POSSIBLE TREATMENT AND ITS RESULTS [J].
GOERZ, G ;
KRIEG, T .
DEUTSCHE MEDIZINISCHE WOCHENSCHRIFT, 1978, 103 (34) :1329-1333
[23]   PORPHYRIA CUTANEA-TARDA - CLINICAL-FEATURES AND LABORATORY FINDINGS IN 40 PATIENTS [J].
GROSSMAN, ME ;
BICKERS, DR ;
POHFITZPATRICK, MB ;
DELEO, VA ;
HARBER, LC .
AMERICAN JOURNAL OF MEDICINE, 1979, 67 (02) :277-286
[24]  
HENNING H, 1976, DIAGNOSTIK, V9, P275
[25]  
HENNING H, 1976, PORPHYRINS HUMAN DIS, P348
[27]   PORPHYRIA CUTANEA-TARDA IN A 2-YEAR-OLD GIRL [J].
KANSKY, A .
BRITISH JOURNAL OF DERMATOLOGY, 1974, 90 (02) :213-216
[28]  
KORDAC V, 1978, DIAGNOSIS THERAPY PO, P127
[29]   INHERITED ENZYMATIC DEFECT IN PORPHYRIA CUTANEA-TARDA - DECREASED UROPORPHYRINOGEN DECARBOXYLASE ACTIVITY [J].
KUSHNER, JP ;
BARBUTO, AJ ;
LEE, GR .
JOURNAL OF CLINICAL INVESTIGATION, 1976, 58 (05) :1089-1097
[30]   INHERITANCE OF PORPHYRIA CUTANEA-TARDA [J].
MCEWIN, R .
MEDICAL JOURNAL OF AUSTRALIA, 1973, 2 (08) :398-399