GLOMERULOCYSTIC DISEASE - UNILATERAL INVOLVEMENT OF A HORSESHOE KIDNEY AND IN TRISOMY-18

被引:9
作者
CRAVER, RD
ORTENBERG, J
BALIGA, R
机构
[1] New Orleans Children's Hospital, Louisiana State University Medical Center, New Orleans, Louisiana
关键词
GLOMERULOCYSTIC DISEASE; AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE; HORSESHOE KIDNEY; TRISOMY-18; RENAL DYSPLASIA;
D O I
10.1007/BF00857542
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Two occurrences of glomerulocystic kidney disease (GCD) in children younger than 1 year are described. One child was 3 months old with trisomy 18; the other child was 6 months old with GCD localized to one side of a horseshoe kidney. Lectin and immunohistochemical studies in tissue from the second child suggested that the entire nephron may be affected in GCD. There may also be overlap of morphological features between GCD and early stages of autosomal dominant polycystic kidneys.
引用
收藏
页码:375 / 378
页数:4
相关论文
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