Systemic capillary leak syndrome

被引：27

作者：

Chihara, R ^{[1
]}

Nakamoto, H ^{[1
]}

Arima, H ^{[1
]}

Moriwaki, K ^{[1
]}

Kanno, Y ^{[1
]}

Sugahara, S ^{[1
]}

Okada, H ^{[1
]}

Suzuki, H ^{[1
]}

机构：

[1] Saitama Med Sch, Dept Nephrol, Moroyama, Saitama 3500495, Japan

来源：

INTERNAL MEDICINE | 2002年 / 41卷 / 11期

关键词：

shock; edema; hypoalbuminemia; pulmonary edema;

D O I：

10.2169/internalmedicine.41.953

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Systemic capillary leak syndrome (SCLS) is characterized by recurrent hypovolemic shock attributable to increased systemic capillary leakage. A 46-year-old man was admitted to our hospital because of recurrent episodes of generalized edema with hypovolemic shock. Blood laboratory data revealed severe hypoproteinemia with a small monoclonal IgG-kappa protein. These findings suggested strongly the diagnosis of SCLS. A regimen with steroid pulse therapy was tried; however, intravascular overloading accompanied by the recruitment of the initially extravasated fluids resulted in acute pulmonary edema. Intensive care and careful monitoring of fluid volume are required in SCLS.

引用

页码：953 / 956

页数：4

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