Systemic capillary leak syndrome

被引:27
作者
Chihara, R [1 ]
Nakamoto, H [1 ]
Arima, H [1 ]
Moriwaki, K [1 ]
Kanno, Y [1 ]
Sugahara, S [1 ]
Okada, H [1 ]
Suzuki, H [1 ]
机构
[1] Saitama Med Sch, Dept Nephrol, Moroyama, Saitama 3500495, Japan
关键词
shock; edema; hypoalbuminemia; pulmonary edema;
D O I
10.2169/internalmedicine.41.953
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Systemic capillary leak syndrome (SCLS) is characterized by recurrent hypovolemic shock attributable to increased systemic capillary leakage. A 46-year-old man was admitted to our hospital because of recurrent episodes of generalized edema with hypovolemic shock. Blood laboratory data revealed severe hypoproteinemia with a small monoclonal IgG-kappa protein. These findings suggested strongly the diagnosis of SCLS. A regimen with steroid pulse therapy was tried; however, intravascular overloading accompanied by the recruitment of the initially extravasated fluids resulted in acute pulmonary edema. Intensive care and careful monitoring of fluid volume are required in SCLS.
引用
收藏
页码:953 / 956
页数:4
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