Development of nonspecific interstitial pneumonitis associated with long-term treatment of primary pulmonary hypertension with prostacyclin

被引:15
作者
Kesten, S [1 ]
Dainauskas, J [1 ]
McLaughlin, V [1 ]
Rich, S [1 ]
机构
[1] Rush Presbyterian St Lukes Med Ctr, Chicago, IL 60612 USA
关键词
interstitial lung disease; primary pulmonary hypertension; prostacyclin;
D O I
10.1378/chest.116.2.566
中图分类号
R4 [临床医学];
学科分类号
1002 ; 100602 ;
摘要
A young woman with primary pulmonary hypertension presented with interstitial lung disease approximately 5 years after successful treatment with IV prostacyclin, The pathology was consistent with nonspecific interstitial pneumonitis and was unresponsive to steroids and immunosuppressive medications. We speculate that further cases of this syndrome may be reported as more patients are living beyond 5 years with prostacyclin.
引用
收藏
页码:566 / 569
页数:4
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