Recurrent hemolytic uremic syndrome with hypocomplementemia and intestinal lymphangiectasia

被引:8
作者
Bogdanovic, R [1 ]
Stankovic, I [1 ]
Jojic, N [1 ]
Ognjanovic, M [1 ]
Zlatkovic, M [1 ]
Popovic, O [1 ]
Nikolic, V [1 ]
机构
[1] ZVEZDARA CLIN CTR, BELGRADE, YUGOSLAVIA
关键词
recurrent hemolytic uremic syndrome; hypocomplementemia; intestinal lymphangiectasia; protein-losing enteropathy;
D O I
10.1159/000190232
中图分类号
R5 [内科学]; R69 [泌尿科学(泌尿生殖系疾病)];
学科分类号
1002 ; 100201 ;
摘要
A 23-year old male patient had eight distinct episodes of hemolytic uremic syndrome (HUS) between 8.5 and 15 years of age, five of them accompanied by hypocomplementemia. In the further course, severe hypertension, renal insufficiency as well as protein-losing enteropathy due to intestinal lymphangiectasia developed, whilst hypocomplementemia persisted. The association of recurrent HUS with hypocomplementemia and intestinal lymphangiectasia may represent a new association within a subgroup of the atypical HUS.
引用
收藏
页码:481 / 484
页数:4
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