Scleromyxedema

被引：32

作者：

Bata-Csorgo, Z

Husz, S

Foldes, M

Korom, I

Molnar, K

Morvay, M

Dobozy, A

机构：

[1] Albert Szent Gyorgyi Med Univ, Dept Dermatol, H-6701 Szeged, Hungary

[2] Univ Michigan, Dept Dermatol, Ann Arbor, MI 48109 USA

来源：

JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY | 1999年 / 41卷 / 02期

关键词：

D O I：

10.1016/S0190-9622(99)70383-X

中图分类号：

R75 [皮肤病学与性病学];

学科分类号：

100206 ;

摘要：

Scleromyxedema is a sclerotic variant of papular mucinosis, in which lichenoid papules and scleroderma-like features are present. We describe a patient with scleromyxedema with IgG type lambda chain paraprotein, a systemic sclerosis-like illness, and myositis. The patient's serum contained Sd 70 antibodies, characteristic of scleroderma. Electromyography showed signs of acute myositis and the creatine phosphokinase (CPK) level was elevated. Multiply passaged fibroblasts from the patient's skin lesions showed altered growth response in vitro. The patient was treated with cyclosporin (4 mg/kg/day) with improvement.

引用

页码：343 / 346

页数：4

共 22 条

[1]

ALLIGOOD TR, 1981, CUTIS, V28, P60

[2] EXTRACORPOREAL PHOTOCHEMOTHERAPY - A POTENTIALLY USEFUL TREATMENT FOR SCLEROMYXEDEMA [J].