Metabolic stroke in methylmalonic acidemia five years after liver transplantation

被引：82

作者：

Chakrapani, A ^{[1
]}

Sivakumar, P

McKiernan, PJ

Leonard, JV

机构：

[1] Birmingham Childrens Hosp, Liver Unit, Birmingham B5 6NH, W Midlands, England

[2] Luton & Dunstable Hosp, Luton, Beds, England

[3] Inst Child Hlth, Biochem Endocrinol & Metab Unit, London, England

来源：

JOURNAL OF PEDIATRICS | 2002年 / 140卷 / 02期

关键词：

D O I：

10.1067/mpd.2002.121698

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

It is believed that Ever transplantation may improve the outcome of early onset methytmalonic acidemia. We report a case of methytmalonic acidemia in which successful liver transplantation in infancy faded to prevent neurologic damage caused by a metabolic stroke.

引用

页码：261 / 263

页数：3

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