Alpha1-antitrypsin deficiency, cirrhosis and emphysema

被引:76
作者
Mahadeva, R
Lomas, DA
机构
[1] Univ Cambridge, MRC Ctr, Dept Med, Resp Med Unit, Cambridge CB2 2QH, England
[2] Univ Cambridge, MRC Ctr, Dept Haematol, Cambridge CB2 2QH, England
关键词
D O I
10.1136/thx.53.6.501
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
[No abstract available]
引用
收藏
页码:501 / 505
页数:5
相关论文
共 61 条
[1]  
*AM THOR SOC, 1986, AM REV RESPIR DIS, V136, P225
[2]  
BEATTY K, 1980, J BIOL CHEM, V255, P3931
[3]  
BRANTLY M, 1988, AM J MED, V84, P13
[4]   THROMBOEMBOLIC DISEASE DUE TO THERMOLABILE CONFORMATIONAL-CHANGES OF ANTITHROMBIN ROUEN-VI (187-ASN-]ASP) [J].
BRUCE, D ;
PERRY, DJ ;
BORG, JY ;
CARRELL, RW ;
WARDELL, MR .
JOURNAL OF CLINICAL INVESTIGATION, 1994, 94 (06) :2265-2274
[5]   POTENTIAL MECHANISM OF EMPHYSEMA - ALPHA-1-PROTEINASE INHIBITOR RECOVERED FROM LUNGS OF CIGARETTE SMOKERS CONTAINS OXIDIZED METHIONINE AND HAS DECREASED ELASTASE INHIBITORY CAPACITY [J].
CARP, H ;
MILLER, F ;
HOIDAL, JR ;
JANOFF, A .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1982, 79 (06) :2041-2045
[6]   Conformational disease [J].
Carrell, RW ;
Lomas, DA .
LANCET, 1997, 350 (9071) :134-138
[7]   BIOLOGICAL IMPLICATIONS OF A 3-ANGSTROM STRUCTURE OF DIMERIC ANTITHROMBIN [J].
CARRELL, RW ;
STEIN, PE ;
WARDELL, MR ;
FERMI, G .
STRUCTURE, 1994, 2 (04) :257-270
[8]   STRUCTURE AND VARIATION OF HUMAN ALPHA-1-ANTITRYPSIN [J].
CARRELL, RW ;
JEPPSSON, JO ;
LAURELL, CB ;
BRENNAN, SO ;
OWEN, MC ;
VAUGHAN, L ;
BOSWELL, DR .
NATURE, 1982, 298 (5872) :329-334
[9]   SYNTHESIS IN ESCHERICHIA-COLI OF ALPHA-1-ANTITRYPSIN VARIANTS OF THERAPEUTIC POTENTIAL FOR EMPHYSEMA AND THROMBOSIS [J].
COURTNEY, M ;
JALLAT, S ;
TESSIER, LH ;
BENAVENTE, A ;
CRYSTAL, RG ;
LECOCQ, JP .
NATURE, 1985, 313 (5998) :149-151
[10]   COOH-TERMINAL SUBSTITUTIONS IN THE SERPIN C1 INHIBITOR THAT CAUSE LOOP OVERINSERTION AND SUBSEQUENT MULTIMERIZATION [J].
ELDERING, E ;
VERPY, E ;
ROEM, D ;
MEO, T ;
TOSI, M .
JOURNAL OF BIOLOGICAL CHEMISTRY, 1995, 270 (06) :2579-2587