Persistent pulmonary hypertension of newborn due to congenital capillary alveolar dysplasia

被引：22

作者：

Singh, SA

Ibrahim, T

Clark, DJ

Taylor, RS

George, DH

机构：

[1] Univ Calgary, Foothills Med Ctr, Dept Pathol, Calgary, AB T2N 2T9, Canada

[2] Univ Calgary, Foothills Med Ctr, Dept Neonatol, Calgary, AB T2N 2T9, Canada

来源：

PEDIATRIC PULMONOLOGY | 2005年 / 40卷 / 04期

关键词：

alveolar capillary dysplasia; persistent pulmonary hypertension; neonate;

D O I：

10.1002/ppul.20244

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Congenital alveolar capillary dysplasia is a rare and fatal cause of pulmonary hypertension in neonates. We report on a term baby with severe pulmonary hypertension unresponsive to high-frequency ventilation and nitric oxide. A diagnosis of alveolar capillary dysplasia was established on autopsy We review the literature regarding pathophysiology, clinical presentations, associated malformations, and treatment trials.

引用

页码：349 / 353

页数：5