The innate immune system in cystic fibrosis lung disease

被引:136
作者
Bals, R
Weiner, DJ
Wilson, JM
机构
[1] Univ Penn, Wistar Inst, Inst Human Gene Therapy, Dept Med, Philadelphia, PA 19104 USA
[2] Univ Penn, Wistar Inst, Inst Human Gene Therapy, Dept Mol & Cellular Engn, Philadelphia, PA 19104 USA
[3] Childrens Hosp Philadelphia, Div Pulm Med, Philadelphia, PA 19104 USA
关键词
D O I
10.1172/JCI6277
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
[No abstract available]
引用
收藏
页码:303 / 307
页数:5
相关论文
共 30 条
[1]  
Accurso F J, 1997, Curr Opin Pulm Med, V3, P400, DOI 10.1097/00063198-199711000-00002
[2]   LOWER RESPIRATORY-INFECTION AND INFLAMMATION IN INFANTS WITH NEWLY-DIAGNOSED CYSTIC-FIBROSIS [J].
ARMSTRONG, DS ;
GRIMWOOD, K ;
CARZINO, R ;
CARLIN, JB ;
OLINSKY, A ;
PHELAN, PD .
BRITISH MEDICAL JOURNAL, 1995, 310 (6994) :1571-1572
[3]   The peptide antibiotic LL-37/hCAP-18 is expressed in epithelia of the human lung where it has broad antimicrobial activity at the airway surface [J].
Bals, R ;
Wang, XR ;
Zasloff, M ;
Wilson, JM .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1998, 95 (16) :9541-9546
[4]   Human β-defensin 2 is a salt-sensitive peptide antibiotic expressed in human lung [J].
Bals, R ;
Wang, XR ;
Wu, ZR ;
Freeman, T ;
Bafna, V ;
Zasloff, M ;
Wilson, JM .
JOURNAL OF CLINICAL INVESTIGATION, 1998, 102 (05) :874-880
[5]   QUALITATIVE AND QUANTITATIVE MICROBIOLOGICAL ANALYSIS OF SPUTA OF 102 PATIENTS WITH CYSTIC-FIBROSIS [J].
BAUERNFEIND, A ;
BERTELE, RM ;
HARMS, K ;
HORL, G ;
JUNGWIRTH, R ;
PETERMULLER, C ;
PRZYKLENK, B ;
WEISSLEINPFISTER, C .
INFECTION, 1987, 15 (04) :270-277
[6]   HBD-1 - A NOVEL BETA-DEFENSIN FROM HUMAN PLASMA [J].
BENSCH, KW ;
RAIDA, M ;
MAGERT, HJ ;
SCHULZKNAPPE, P ;
FORSSMANN, WG .
FEBS LETTERS, 1995, 368 (02) :331-335
[7]  
Berger M, 1999, CYSTIC FIBROSIS IN ADULTS, P115
[8]   TRACHEAL ANTIMICROBIAL PEPTIDE, A CYSTEINE-RICH PEPTIDE FROM MAMMALIAN TRACHEAL MUCOSA - PEPTIDE ISOLATION AND CLONING OF A CDNA [J].
DIAMOND, G ;
ZASLOFF, M ;
ECK, H ;
BRASSEUR, M ;
MALOY, WL ;
BEVINS, CL .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1991, 88 (09) :3952-3956
[9]   Elements of immunity - The instructive role of innate immunity in the acquired immune response [J].
Fearon, DT ;
Locksley, RM .
SCIENCE, 1996, 272 (5258) :50-54
[10]   DEFENSINS [J].
GANZ, T ;
LEHRER, RI .
PHARMACOLOGY & THERAPEUTICS, 1995, 66 (02) :191-205