共 35 条
Fukutin is required for maintenance of muscle integrity, cortical histiogenesis and normal eye development
被引:82
作者:

Takeda, S
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Postgenom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Kondo, M
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Postgenom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Sasaki, J
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Postgenom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Kurahashi, H
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Postgenom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Kano, H
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Postgenom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Arai, K
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Postgenom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Misaki, K
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Postgenom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

论文数: 引用数:
h-index:
机构:

Kobayashi, K
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Postgenom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Tachikawa, M
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Postgenom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Imamura, M
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Postgenom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Nakamura, Y
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Postgenom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

论文数: 引用数:
h-index:
机构:

Murakami, T
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Postgenom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Sunada, Y
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Postgenom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Fujikado, T
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Postgenom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Matsumura, K
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Postgenom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Terashima, T
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Postgenom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Toda, T
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Postgenom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan
机构:
[1] Osaka Univ, Grad Sch Med, Dept Postgenom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan
[2] Otsuka Pharmaceut Co Ltd, Otsuka GEN Res Inst, Tokushima 77101, Japan
[3] Teikyo Univ, Sch Med, Dept Neurol, Tokyo 173, Japan
[4] Kobe Univ, Grad Sch Med, Dept Anat & Neurobiol, Kobe, Hyogo 657, Japan
[5] Osaka Univ, Grad Sch Med, Dept Ophthalmol & Visual Sci, Osaka, Japan
[6] Natl Ctr Neurol & Psychiat, Inst Neurosci, Tokyo, Japan
[7] Univ Tokyo, Inst Med Sci, Ctr Human Genome, Tokyo, Japan
[8] Kawasaki Med Sch, Dept Neurol, Kurashiki, Okayama, Japan
关键词:
D O I:
10.1093/hmg/ddg153
中图分类号:
Q5 [生物化学];
Q7 [分子生物学];
学科分类号:
071010 ;
081704 ;
摘要:
Fukuyama-type congenital muscular dystrophy (FCMD), one of the most common autosomal-recessive disorders in Japan, is characterized by congenital muscular dystrophy associated with brain malformation due to a defect during neuronal migration. Through positional cloning, we previously identified the gene for FCMD, which encodes the fukutin protein. Here we report that chimeric mice generated using embryonic stem cells targeted for both fukutin alleles develop severe muscular dystrophy, with the selective deficiency of alpha-dystroglycan and its laminin-binding activity. In addition, these mice showed laminar disorganization of the cortical structures in the brain with impaired laminin assembly, focal interhemispheric fusion, and hippocampal and cerebellar dysgenesis. Further, chimeric mice showed anomaly of the lens, loss of laminar structure in the retina, and retinal detachment. These results indicate that fukutin is necessary for the maintenance of muscle integrity, cortical histiogenesis, and normal ocular development and suggest the functional linkage between fukutin and alpha-dystroglycan.
引用
收藏
页码:1449 / 1459
页数:11
相关论文
共 35 条
[21]
PRIMARY STRUCTURE OF DYSTROPHIN-ASSOCIATED GLYCOPROTEINS LINKING DYSTROPHIN TO THE EXTRACELLULAR-MATRIX
[J].
IBRAGHIMOVBESKROVNAYA, O
;
ERVASTI, JM
;
LEVEILLE, CJ
;
SLAUGHTER, CA
;
SERNETT, SW
;
CAMPBELL, KP
.
NATURE,
1992, 355 (6362)
:696-702

IBRAGHIMOVBESKROVNAYA, O
论文数: 0 引用数: 0
h-index: 0
机构: UNIV IOWA,COLL MED,HOWARD HUGHES MED INST,IOWA CITY,IA 52242

ERVASTI, JM
论文数: 0 引用数: 0
h-index: 0
机构: UNIV IOWA,COLL MED,HOWARD HUGHES MED INST,IOWA CITY,IA 52242

LEVEILLE, CJ
论文数: 0 引用数: 0
h-index: 0
机构: UNIV IOWA,COLL MED,HOWARD HUGHES MED INST,IOWA CITY,IA 52242

SLAUGHTER, CA
论文数: 0 引用数: 0
h-index: 0
机构: UNIV IOWA,COLL MED,HOWARD HUGHES MED INST,IOWA CITY,IA 52242

SERNETT, SW
论文数: 0 引用数: 0
h-index: 0
机构: UNIV IOWA,COLL MED,HOWARD HUGHES MED INST,IOWA CITY,IA 52242

CAMPBELL, KP
论文数: 0 引用数: 0
h-index: 0
机构: UNIV IOWA,COLL MED,HOWARD HUGHES MED INST,IOWA CITY,IA 52242
[22]
A sarcoglycan-dystroglycan complex anchors Dp116 and utrophin in the peripheral nervous system
[J].
Imamura, M
;
Araishi, K
;
Noguchi, S
;
Ozawa, E
.
HUMAN MOLECULAR GENETICS,
2000, 9 (20)
:3091-3100

Imamura, M
论文数: 0 引用数: 0
h-index: 0
机构: Natl Ctr Neurol & Psychiat, Natl Inst Neurosci, Dept Cell Biol, Tokyo 1878502, Japan

Araishi, K
论文数: 0 引用数: 0
h-index: 0
机构: Natl Ctr Neurol & Psychiat, Natl Inst Neurosci, Dept Cell Biol, Tokyo 1878502, Japan

论文数: 引用数:
h-index:
机构:

Ozawa, E
论文数: 0 引用数: 0
h-index: 0
机构: Natl Ctr Neurol & Psychiat, Natl Inst Neurosci, Dept Cell Biol, Tokyo 1878502, Japan
[23]
Deficiency of α-dystroglycan in muscle-eye-brain disease
[J].
Kano, H
;
Kobayashi, K
;
Herrmann, R
;
Tachikawa, M
;
Manya, H
;
Nishino, I
;
Nonaka, I
;
Straub, V
;
Talim, B
;
Voit, T
;
Topaloglu, H
;
Endo, T
;
Yoshikawa, H
;
Toda, T
.
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
2002, 291 (05)
:1283-1286

Kano, H
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Post Genom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Kobayashi, K
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Post Genom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Herrmann, R
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Post Genom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Tachikawa, M
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Post Genom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Manya, H
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Post Genom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

论文数: 引用数:
h-index:
机构:

Nonaka, I
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Post Genom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Straub, V
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Post Genom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Talim, B
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Post Genom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Voit, T
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Post Genom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Topaloglu, H
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Post Genom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Endo, T
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Post Genom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Yoshikawa, H
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Post Genom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan

Toda, T
论文数: 0 引用数: 0
h-index: 0
机构: Osaka Univ, Grad Sch Med, Dept Post Genom & Dis, Div Funct Genom, Suita, Osaka 5650871, Japan
[24]
An ancient retrotransposal insertion causes Fukuyama-type congenital muscular dystrophy
[J].
Kobayashi, K
;
Nakahori, Y
;
Miyake, M
;
Matsumura, K
;
Kondo-Iida, E
;
Nomura, Y
;
Segawa, M
;
Yoshioka, M
;
Saito, K
;
Osawa, K
;
Hamano, K
;
Sakakihara, Y
;
Nonaka, I
;
Nakagome, Y
;
Kanazawa, I
;
Nakamura, Y
;
Tokunaga, K
;
Toda, T
.
NATURE,
1998, 394 (6691)
:388-392

Kobayashi, K
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Nakahori, Y
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Miyake, M
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Matsumura, K
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Kondo-Iida, E
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Nomura, Y
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Segawa, M
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Yoshioka, M
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Saito, K
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Osawa, K
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Hamano, K
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Sakakihara, Y
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Nonaka, I
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Nakagome, Y
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Kanazawa, I
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Nakamura, Y
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Tokunaga, K
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Toda, T
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan
[25]
Novel mutations and genotype-phenotype relationships in 107 families with Fukuyama-type congenital muscular dystrophy (FCMD)
[J].
Kondo-Iida, E
;
Kobayashi, K
;
Watanabe, M
;
Sasaki, J
;
Kumagai, T
;
Koide, H
;
Saito, K
;
Osawa, M
;
Nakamura, Y
;
Toda, T
.
HUMAN MOLECULAR GENETICS,
1999, 8 (12)
:2303-2309

Kondo-Iida, E
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Kobayashi, K
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Watanabe, M
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Sasaki, J
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Kumagai, T
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Koide, H
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Saito, K
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Osawa, M
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Nakamura, Y
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan

Toda, T
论文数: 0 引用数: 0
h-index: 0
机构: Univ Tokyo, Inst Med Sci, Ctr Human Genome, Lab Genome Med,Minato Ku, Tokyo 1088639, Japan
[26]
A role of dystroglycan in schwannoma cell adhesion to laminin
[J].
Matsumura, K
;
Chiba, A
;
Yamada, H
;
FukutaOhi, H
;
Fujita, S
;
Endo, T
;
Kobata, A
;
Anderson, LVB
;
Kanazawa, I
;
Campbell, KP
;
Shimizu, T
.
JOURNAL OF BIOLOGICAL CHEMISTRY,
1997, 272 (21)
:13904-13910

Matsumura, K
论文数: 0 引用数: 0
h-index: 0
机构: TEIKYO UNIV,SCH MED,DEPT NEUROL & NEUROSCI,TOKYO 173,JAPAN

Chiba, A
论文数: 0 引用数: 0
h-index: 0
机构: TEIKYO UNIV,SCH MED,DEPT NEUROL & NEUROSCI,TOKYO 173,JAPAN

Yamada, H
论文数: 0 引用数: 0
h-index: 0
机构: TEIKYO UNIV,SCH MED,DEPT NEUROL & NEUROSCI,TOKYO 173,JAPAN

FukutaOhi, H
论文数: 0 引用数: 0
h-index: 0
机构: TEIKYO UNIV,SCH MED,DEPT NEUROL & NEUROSCI,TOKYO 173,JAPAN

Fujita, S
论文数: 0 引用数: 0
h-index: 0
机构: TEIKYO UNIV,SCH MED,DEPT NEUROL & NEUROSCI,TOKYO 173,JAPAN

Endo, T
论文数: 0 引用数: 0
h-index: 0
机构: TEIKYO UNIV,SCH MED,DEPT NEUROL & NEUROSCI,TOKYO 173,JAPAN

Kobata, A
论文数: 0 引用数: 0
h-index: 0
机构: TEIKYO UNIV,SCH MED,DEPT NEUROL & NEUROSCI,TOKYO 173,JAPAN

Anderson, LVB
论文数: 0 引用数: 0
h-index: 0
机构: TEIKYO UNIV,SCH MED,DEPT NEUROL & NEUROSCI,TOKYO 173,JAPAN

Kanazawa, I
论文数: 0 引用数: 0
h-index: 0
机构: TEIKYO UNIV,SCH MED,DEPT NEUROL & NEUROSCI,TOKYO 173,JAPAN

Campbell, KP
论文数: 0 引用数: 0
h-index: 0
机构: TEIKYO UNIV,SCH MED,DEPT NEUROL & NEUROSCI,TOKYO 173,JAPAN

Shimizu, T
论文数: 0 引用数: 0
h-index: 0
机构: TEIKYO UNIV,SCH MED,DEPT NEUROL & NEUROSCI,TOKYO 173,JAPAN
[27]
DEFICIENCY OF THE 50K DYSTROPHIN-ASSOCIATED GLYCOPROTEIN IN SEVERE CHILDHOOD AUTOSOMAL RECESSIVE MUSCULAR-DYSTROPHY
[J].
MATSUMURA, K
;
TOME, FMS
;
COLLIN, H
;
AZIBI, K
;
CHAOUCH, M
;
KAPLAN, JC
;
FARDEAU, M
;
CAMPBELL, KP
.
NATURE,
1992, 359 (6393)
:320-322

MATSUMURA, K
论文数: 0 引用数: 0
h-index: 0
机构: UNIV IOWA, COLL MED, HOWARD HUGHES MED INST, IOWA CITY, IA 52242 USA

TOME, FMS
论文数: 0 引用数: 0
h-index: 0
机构: UNIV IOWA, COLL MED, HOWARD HUGHES MED INST, IOWA CITY, IA 52242 USA

COLLIN, H
论文数: 0 引用数: 0
h-index: 0
机构: UNIV IOWA, COLL MED, HOWARD HUGHES MED INST, IOWA CITY, IA 52242 USA

AZIBI, K
论文数: 0 引用数: 0
h-index: 0
机构: UNIV IOWA, COLL MED, HOWARD HUGHES MED INST, IOWA CITY, IA 52242 USA

CHAOUCH, M
论文数: 0 引用数: 0
h-index: 0
机构: UNIV IOWA, COLL MED, HOWARD HUGHES MED INST, IOWA CITY, IA 52242 USA

KAPLAN, JC
论文数: 0 引用数: 0
h-index: 0
机构: UNIV IOWA, COLL MED, HOWARD HUGHES MED INST, IOWA CITY, IA 52242 USA

FARDEAU, M
论文数: 0 引用数: 0
h-index: 0
机构: UNIV IOWA, COLL MED, HOWARD HUGHES MED INST, IOWA CITY, IA 52242 USA

CAMPBELL, KP
论文数: 0 引用数: 0
h-index: 0
机构: UNIV IOWA, COLL MED, HOWARD HUGHES MED INST, IOWA CITY, IA 52242 USA
[28]
TETRAMETHYL BENZIDINE FOR HORSERADISH-PEROXIDASE NEURO-HISTOCHEMISTRY - NON-CARCINOGENIC BLUE REACTION-PRODUCT WITH SUPERIOR SENSITIVITY FOR VISUALIZING NEURAL AFFERENTS AND EFFERENTS
[J].
MESULAM, MM
.
JOURNAL OF HISTOCHEMISTRY & CYTOCHEMISTRY,
1978, 26 (02)
:106-117

MESULAM, MM
论文数: 0 引用数: 0
h-index: 0
[29]
Post-translational disruption of dystroglycan-ligand interactions in congenital muscular dystrophies
[J].
Michele, DE
;
Barresi, R
;
Kanagawa, M
;
Saito, F
;
Cohn, RD
;
Satz, JS
;
Dollar, J
;
Nishino, I
;
Kelley, RI
;
Somer, H
;
Straub, V
;
Mathews, KD
;
Moore, SA
;
Campbell, KP
.
NATURE,
2002, 418 (6896)
:417-422

Michele, DE
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

Barresi, R
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

Kanagawa, M
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

Saito, F
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

Cohn, RD
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

Satz, JS
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

Dollar, J
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

论文数: 引用数:
h-index:
机构:

Kelley, RI
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

Somer, H
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

Straub, V
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

Mathews, KD
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

Moore, SA
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

Campbell, KP
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA
[30]
Deletion of brain dystroglycan recapitulates aspects of congenital muscular dystrophy
[J].
Moore, SA
;
Saito, F
;
Chen, JG
;
Michele, DE
;
Henry, MD
;
Messing, A
;
Cohn, RD
;
Ross-Barta, SE
;
Westra, S
;
Williamson, RA
;
Hoshi, T
;
Campbell, KP
.
NATURE,
2002, 418 (6896)
:422-425

Moore, SA
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

Saito, F
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

Chen, JG
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

Michele, DE
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

Henry, MD
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

Messing, A
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

Cohn, RD
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

Ross-Barta, SE
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

Westra, S
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

Williamson, RA
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

Hoshi, T
论文数: 0 引用数: 0
h-index: 0
机构: Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA

Campbell, KP
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA Univ Iowa, Howard Hughes Med Inst, Dept Physiol & Biophys, Iowa City, IA 52242 USA