Prion diseases: Transmission from mad cows?

被引:7
作者
Roberts, GW
James, S
机构
[1] Dept. of Molec. Neuropathology Res., SmithKline Beecham Pharmaceut. Ltd., Harlow, Essex, CM19 5AW, New Front. Sci. Pk., N. Third Ave.
关键词
D O I
10.1016/S0960-9822(02)70708-2
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
Prion diseases in humans show considerable clinical and pathological heterogeneity. The identification of a new variant of Creutzfeldt-Jakob disease, and its interpretation as evidence of transmission of mad cow disease to man, rely critically on our understanding of the epidemiology of prion diseases.
引用
收藏
页码:1247 / 1249
页数:3
相关论文
共 13 条
  • [1] NONGENETIC PROPAGATION OF STRAIN-SPECIFIC PROPERTIES OF SCRAPIE PRION PROTEIN
    BESSEN, RA
    KOCISKO, DA
    RAYMOND, GJ
    NANDAN, S
    LANSBURY, PT
    CAUGHEY, B
    [J]. NATURE, 1995, 375 (6533) : 698 - 700
  • [2] Normal host prion protein necessary for scrapie-induced neurotoxicity
    Brandner, S
    Isenmann, S
    Raeber, A
    Fischer, M
    Sailer, A
    Kobayashi, Y
    Marino, S
    Weissmann, C
    Aguzzi, A
    [J]. NATURE, 1996, 379 (6563) : 339 - 343
  • [3] Diagnosis and incidence of prion (Creutzfeldt-Jakob) disease: A retrospective archival survey with implications for future research
    Bruton, CJ
    Bruton, RK
    Gentleman, SM
    Roberts, GW
    [J]. NEURODEGENERATION, 1995, 4 (04): : 357 - 368
  • [4] LIFE, JIM, BUT NOT AS WE KNOW IT - TRANSMISSIBLE DEMENTIAS AND THE PRION PROTEIN
    HARRISON, PJ
    ROBERTS, GW
    [J]. BRITISH JOURNAL OF PSYCHIATRY, 1991, 158 : 457 - 470
  • [5] The double life of the prion protein
    Lansbury, PT
    Caughey, B
    [J]. CURRENT BIOLOGY, 1996, 6 (08) : 914 - 916
  • [6] *NAT CJD SURV UN, 1995, 4 NAT CJD SURV UN DE
  • [7] HOMOZYGOUS PRION PROTEIN GENOTYPE PREDISPOSES TO SPORADIC CREUTZFELDT-JAKOB DISEASE
    PALMER, MS
    DRYDEN, AJ
    HUGHES, JT
    COLLINGE, J
    [J]. NATURE, 1991, 352 (6333) : 340 - 342
  • [8] Molecular basis of phenotypic variability in sporadic Creutzfeldt-Jakob disease
    Parchi, P
    Castellani, R
    Capellari, S
    Ghetti, B
    Young, K
    Chen, SG
    Farlow, M
    Dickson, DW
    Sima, AAF
    Trojanowski, JQ
    Petersen, RB
    Gambetti, P
    [J]. ANNALS OF NEUROLOGY, 1996, 39 (06) : 767 - 778
  • [9] PRION DISEASES AND NEURODEGENERATION
    PRUSINER, SB
    DEARMOND, SJ
    [J]. ANNUAL REVIEW OF NEUROSCIENCE, 1994, 17 : 311 - 339
  • [10] THE NOSOLOGY OF CREUTZFELDT-JAKOB-DISEASE AND CONDITIONS RELATED TO THE ACCUMULATION OF PRPCJD IN THE NERVOUS-SYSTEM
    RICHARDSON, EP
    MASTERS, CL
    [J]. BRAIN PATHOLOGY, 1995, 5 (01) : 33 - 41