A select group of microorganisms inhabit the airways of individuals with cystic fibrosis. Once established within the pulmonary environment in these patients, many of these microbes adapt by altering aspects of their structure and physiology. Some of these microbes and adaptations are associated with more rapid deterioration in lung function and overall clinical status, whereas others appear to have little effect. Here we review current evidence supporting or refuting a role for the different microbes and their adaptations in contributing to poor clinical outcomes in cystic fibrosis.
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Boles BR, 2004, P NATL ACAD SCI USA, V101, P16630, DOI 10.1073/pnas.0407460101
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HEGP, AP HP, Pole Cardio Thorac, Paris, FranceHEGP, AP HP, Pole Cardio Thorac, Paris, France
Boussaud, V.
Guillemain, R.
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HEGP, AP HP, Dept Anesthesie Reanimat, Paris, FranceHEGP, AP HP, Pole Cardio Thorac, Paris, France
Guillemain, R.
Grenet, D.
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Hop Foch, Pole Malad Resp, Suresnes, FranceHEGP, AP HP, Pole Cardio Thorac, Paris, France
Grenet, D.
Coley, N.
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机构:HEGP, AP HP, Pole Cardio Thorac, Paris, France
Coley, N.
Souilamas, R.
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HEGP, AP HP, Pole Cardio Thorac, Paris, France
Hop Purpan, Inst Fed Biol, Observ Cepacia Lab Bacteriol Hyg, Toulouse, FranceHEGP, AP HP, Pole Cardio Thorac, Paris, France
Souilamas, R.
Bonnette, P.
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Hop Foch, Pole Malad Resp, Suresnes, FranceHEGP, AP HP, Pole Cardio Thorac, Paris, France
Bonnette, P.
Stern, M.
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Hop Foch, Pole Malad Resp, Suresnes, FranceHEGP, AP HP, Pole Cardio Thorac, Paris, France
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Ist Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, ItalyIst Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, Italy
Bragonzi, Alessandra
Paroni, Moira
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Ist Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, ItalyIst Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, Italy
Paroni, Moira
Nonis, Alessandro
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Univ Vita Salute San Raffaele, Univ Ctr Stat Biomed Sci, Milan, ItalyIst Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, Italy
Nonis, Alessandro
Cramer, Nina
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Hannover Med Sch, Klin Forschergrp, OE 6710, D-30623 Hannover, GermanyIst Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, Italy
Cramer, Nina
Montanari, Sara
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Ist Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, ItalyIst Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, Italy
Montanari, Sara
Rejman, Joanna
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Ist Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, ItalyIst Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, Italy
Rejman, Joanna
Di Serio, Clelia
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Univ Vita Salute San Raffaele, Univ Ctr Stat Biomed Sci, Milan, ItalyIst Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, Italy
Di Serio, Clelia
Doering, Gerd
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Univ Klinikum Tubingen, Inst Med Microbiol & Hyg, Tubingen, GermanyIst Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, Italy
Doering, Gerd
Tuemmler, Burkhard
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Hannover Med Sch, Klin Forschergrp, OE 6710, D-30623 Hannover, GermanyIst Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, Italy
机构:
HEGP, AP HP, Pole Cardio Thorac, Paris, FranceHEGP, AP HP, Pole Cardio Thorac, Paris, France
Boussaud, V.
Guillemain, R.
论文数: 0引用数: 0
h-index: 0
机构:
HEGP, AP HP, Dept Anesthesie Reanimat, Paris, FranceHEGP, AP HP, Pole Cardio Thorac, Paris, France
Guillemain, R.
Grenet, D.
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h-index: 0
机构:
Hop Foch, Pole Malad Resp, Suresnes, FranceHEGP, AP HP, Pole Cardio Thorac, Paris, France
Grenet, D.
Coley, N.
论文数: 0引用数: 0
h-index: 0
机构:HEGP, AP HP, Pole Cardio Thorac, Paris, France
Coley, N.
Souilamas, R.
论文数: 0引用数: 0
h-index: 0
机构:
HEGP, AP HP, Pole Cardio Thorac, Paris, France
Hop Purpan, Inst Fed Biol, Observ Cepacia Lab Bacteriol Hyg, Toulouse, FranceHEGP, AP HP, Pole Cardio Thorac, Paris, France
Souilamas, R.
Bonnette, P.
论文数: 0引用数: 0
h-index: 0
机构:
Hop Foch, Pole Malad Resp, Suresnes, FranceHEGP, AP HP, Pole Cardio Thorac, Paris, France
Bonnette, P.
Stern, M.
论文数: 0引用数: 0
h-index: 0
机构:
Hop Foch, Pole Malad Resp, Suresnes, FranceHEGP, AP HP, Pole Cardio Thorac, Paris, France
机构:
Ist Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, ItalyIst Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, Italy
Bragonzi, Alessandra
Paroni, Moira
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h-index: 0
机构:
Ist Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, ItalyIst Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, Italy
Paroni, Moira
Nonis, Alessandro
论文数: 0引用数: 0
h-index: 0
机构:
Univ Vita Salute San Raffaele, Univ Ctr Stat Biomed Sci, Milan, ItalyIst Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, Italy
Nonis, Alessandro
Cramer, Nina
论文数: 0引用数: 0
h-index: 0
机构:
Hannover Med Sch, Klin Forschergrp, OE 6710, D-30623 Hannover, GermanyIst Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, Italy
Cramer, Nina
Montanari, Sara
论文数: 0引用数: 0
h-index: 0
机构:
Ist Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, ItalyIst Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, Italy
Montanari, Sara
Rejman, Joanna
论文数: 0引用数: 0
h-index: 0
机构:
Ist Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, ItalyIst Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, Italy
Rejman, Joanna
Di Serio, Clelia
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h-index: 0
机构:
Univ Vita Salute San Raffaele, Univ Ctr Stat Biomed Sci, Milan, ItalyIst Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, Italy
Di Serio, Clelia
Doering, Gerd
论文数: 0引用数: 0
h-index: 0
机构:
Univ Klinikum Tubingen, Inst Med Microbiol & Hyg, Tubingen, GermanyIst Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, Italy
Doering, Gerd
Tuemmler, Burkhard
论文数: 0引用数: 0
h-index: 0
机构:
Hannover Med Sch, Klin Forschergrp, OE 6710, D-30623 Hannover, GermanyIst Sci San Raffaele, Infect & Cyst Fibrosis Unit, Div Immunol Transplantat & Infect Dis, I-20132 Milan, Italy