Management of pregnancy in a patient with severe haemophilia A

被引:17
作者
Dhar, P [1 ]
Abramovitz, S [1 ]
DiMichele, D [1 ]
Gibb, CB [1 ]
Gadalla, F [1 ]
机构
[1] Cornell Univ, New York Presbyterian Hosp, Weill Med Coll, New York, NY USA
关键词
analgesic techniques; epidural; blood; coagulation factor; complications; haemophilia;
D O I
10.1093/bja/aeg177
中图分类号
R614 [麻醉学];
学科分类号
100217 ;
摘要
Haemophilia A is a bleeding disorder that has a spectrum of manifestations ranging from persistent bleeding after minor trauma to spontaneous haemorrhage. As an X-linked disease, it has a rare occurrence in females. We report a case of a pregnant patient with severe haemophilia A, who received epidural analgesia during labour. The prepartum, intrapartum and postpartum care of a patient with such a bleeding diathesis is discussed.
引用
收藏
页码:432 / 435
页数:4
相关论文
共 22 条
  • [11] Pregnancy in women with von Willebrand's disease or factor XI deficiency
    Kadir, RA
    Lee, CA
    Sabin, CA
    Pollard, D
    Economides, DL
    [J]. BRITISH JOURNAL OF OBSTETRICS AND GYNAECOLOGY, 1998, 105 (03): : 314 - 321
  • [12] Le Marec B, 1985, J Genet Hum, V33, P449
  • [13] LYON M, 1978, AM J MED, V65, P637
  • [14] Medical progress - The hemophilias - From royal genes to gene therapy
    Mannucci, PM
    Tuddenham, EGD
    [J]. NEW ENGLAND JOURNAL OF MEDICINE, 2001, 344 (23) : 1773 - 1779
  • [15] A CHROMOSOMAL FEMALE WITH HEMOPHILIA A
    MELLMAN, WJ
    WURZEL, HA
    MOORHEAD, PS
    QUALLS, DH
    WOLMAN, IJ
    [J]. BLOOD, 1961, 17 (06) : 719 - &
  • [16] HEMOPHILIA-A IN A 46,X,I(XQ) FEMALE
    MORI, PG
    PASINO, M
    VADALA, CR
    BISOGNI, MC
    TONINI, GP
    SCARABICCHI, S
    [J]. BRITISH JOURNAL OF HAEMATOLOGY, 1979, 43 (01) : 143 - &
  • [17] NONRANDOM X-CHROMOSOME DNA METHYLATION PATTERNS IN HEMOPHILIAC FEMALES
    NISEN, PD
    WABER, PG
    [J]. JOURNAL OF CLINICAL INVESTIGATION, 1989, 83 (04) : 1400 - 1403
  • [18] Recombinant coagulation factors
    Roddie, PH
    Ludlam, CA
    [J]. BLOOD REVIEWS, 1997, 11 (04) : 169 - 177
  • [19] ABSENCE OF HEPATITIS AFTER TREATMENT WITH A PASTEURIZED FACTOR-VIII CONCENTRATE IN PATIENTS WITH HEMOPHILIA AND NO PREVIOUS TRANSFUSIONS
    SCHIMPF, K
    MANNUCCI, PM
    KREUTZ, W
    BRACKMANN, HH
    AUERSWALD, G
    CIAVARELLA, N
    MOSSELER, J
    DEROSA, V
    KRAUS, B
    BRUECKMANN, C
    MANCUSO, G
    MITTLER, U
    HASCHKE, F
    MORFINI, M
    [J]. NEW ENGLAND JOURNAL OF MEDICINE, 1987, 316 (15) : 918 - 922
  • [20] MRI of acute spinal epidural hematomas
    Sklar, EML
    Post, JMD
    Falcone, S
    [J]. JOURNAL OF COMPUTER ASSISTED TOMOGRAPHY, 1999, 23 (02) : 238 - 243