Rare diseases - 1 - Lymphangioleiomyomatosis: clinical features, management and basic mechanisms

被引:131
作者
Johnson, S [1 ]
机构
[1] Univ Nottingham, City Hosp, Div Resp Med, Nottingham NG5 1PB, England
关键词
D O I
10.1136/thx.54.3.254
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
[No abstract available]
引用
收藏
页码:254 / 264
页数:11
相关论文
共 106 条
[12]   Pulmonary Langerhans cell histiocytosis: Evolution of lesions on CT scans [J].
Brauner, MW ;
Grenier, P ;
Tijani, K ;
Battesti, JP ;
Valeyre, D .
RADIOLOGY, 1997, 204 (02) :497-502
[13]   STEROID-RECEPTORS IN PULMONARY LYMPHANGIOMYOMATOSIS [J].
BRENTANI, MM ;
CARVALHO, CRR ;
SALDIVA, PH ;
PACHECO, MM ;
OSHIMA, CTF .
CHEST, 1984, 85 (01) :96-99
[14]   Pregnancy exacerbating unsuspected mediastinal lymphangioleiomyomatosis and chylothorax [J].
Brunelli, A ;
Catalini, G ;
Fianchini, A .
INTERNATIONAL JOURNAL OF GYNECOLOGY & OBSTETRICS, 1996, 52 (03) :289-290
[15]   THE SMALL GTPASE RAB5 FUNCTIONS AS A REGULATORY FACTOR IN THE EARLY ENDOCYTIC PATHWAY [J].
BUCCI, C ;
PARTON, RG ;
MATHER, IH ;
STUNNENBERG, H ;
SIMONS, K ;
HOFLACK, B ;
ZERIAL, M .
CELL, 1992, 70 (05) :715-728
[16]   PULMONARY MECHANICS IN LYMPHANGIOLEIOMYOMATOSIS [J].
BURGER, CD ;
HYATT, RE ;
STAATS, BA .
AMERICAN REVIEW OF RESPIRATORY DISEASE, 1991, 143 (05) :1030-1033
[17]   Lymphangioleiomyomatosis, chylous ascites, and diet [J].
Calvo, E ;
Amarillas, L ;
Mateos, MA ;
Orradre, JL ;
Gilsanz, G ;
AlvarezSala, JL ;
Espinos, D .
DIGESTIVE DISEASES AND SCIENCES, 1996, 41 (03) :591-593
[18]  
CAMAGGI CM, 1983, CANCER CHEMOTH PHARM, V11, P19
[19]   PULMONARY TUBEROUS SCLEROSIS [J].
CASTRO, M ;
SHEPHERD, CW ;
GOMEZ, MR ;
LIE, JT ;
RYU, JH .
CHEST, 1995, 107 (01) :189-195
[20]   LYMPHANGIOMYOMATOSIS AND ANGIOMYOLIPOMA - CLOSELY RELATED ENTITIES CHARACTERIZED BY HAMARTOMATOUS PROLIFERATION OF HMB-45-POSITIVE SMOOTH-MUSCLE [J].
CHAN, JKC ;
TSANG, WYW ;
PAU, MY ;
TANG, MC ;
PANG, SW ;
FLETCHER, CDM .
HISTOPATHOLOGY, 1993, 22 (05) :445-455