Long QT syndrome: novel insights into the mechanisms of cardiac arrhythmias

被引:92
作者
Kass, RS
Moss, AJ
机构
[1] Columbia Univ, Coll Phys & Surg, Dept Pharmacol, New York, NY 10032 USA
[2] Univ Rochester, Sch Med & Dent, Dept Med, Heart Res Follow Up Program, Rochester, NY 14642 USA
关键词
D O I
10.1172/JCI200319844
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
The congenital long QT syndrome is a rare disorder in which mutation carriers are at risk for polymorphic ventricular tachycardia and/or sudden cardiac death. Discovery and analysis of gene mutations associated with variants of this disorder have provided novel insight into mechanisms of cardiac arrhythmia and have raised the possibility of mutation-specific therapeutic intervention.
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页码:810 / 815
页数:6
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