Genetic diseases of bilirubin metabolism: The inherited unconjugated hyperbilirubinemias

被引:7
作者
Jansen, PLM
机构
[1] Div. of Gastroenterol. and Liver D., University Hospital, Groningen
[2] Div. of Gastroenterol. and Liver D., University Hospital Groningen, NL-9713 GZ Groningen
关键词
D O I
10.1016/S0168-8278(96)80129-2
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
[No abstract available]
引用
收藏
页码:398 / 404
页数:7
相关论文
共 59 条
[21]   CRIGLER-NAJJAR TYPE-1 SYNDROME - ABSENCE OF HEPATIC BILIRUBIN UDP-GLUCURONYL TRANSFERASE-ACTIVITY AND THERAPEUTIC RESPONSE TO LIGHT [J].
FARRELL, GC ;
GOLLAN, JL ;
STEVENS, SMB ;
GRIERSON, JM .
AUSTRALIAN AND NEW ZEALAND JOURNAL OF MEDICINE, 1982, 12 (04) :280-285
[22]   UNCONJUGATED BILIRUBIN AND AN INCREASED PROPORTION OF BILIRUBIN MONO-CONJUGATES IN BILE OF PATIENTS WITH GILBERTS SYNDROME AND CRIGLER-NAJJAR DISEASE [J].
FEVERY, J ;
BLANCKAERT, N ;
HEIRWEGH, KPM ;
PREAUX, AM ;
BERTHELOT, P .
JOURNAL OF CLINICAL INVESTIGATION, 1977, 60 (05) :970-979
[23]  
GENTILE S, 1986, HEPATO-GASTROENTEROL, V33, P155
[24]   CONGENITAL NONOBSTRUCTIVE, NONHEMOLYTIC JAUNDICE . EFFECT OF PHOTOTHERAPY [J].
GORODISCHER, R ;
LEVY, G ;
KRASNER, J ;
YAFFE, SJ .
NEW ENGLAND JOURNAL OF MEDICINE, 1970, 282 (07) :375-+
[25]   CLONING AND SUBSTRATE-SPECIFICITY OF A HUMAN PHENOL UDP-GLUCURONOSYLTRANSFERASE EXPRESSED IN COS-7 CELLS [J].
HARDING, D ;
FOURNELGIGLEUX, S ;
JACKSON, MR ;
BURCHELL, B .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1988, 85 (22) :8381-8385
[26]  
HUANG PWH, 1970, ARCH PATHOL, V90, P536
[27]   CRIGLER-NAJJAR SYNDROME TYPE-I - MANAGEMENT WITH A PHOTOTHERAPY CRIB MATTRESS [J].
HUGHESBENZIE, R ;
UTTLEY, DA ;
HEICK, HMC .
ARCHIVES OF DISEASE IN CHILDHOOD, 1993, 69 (04) :470-470
[28]   INHERITANCE OF TYPE 2 CRIGLER-NAJJAR HYPERBILIRUBINEMIA [J].
HUNTER, JO ;
THOMPSON, RP ;
DUNN, PM ;
WILLIAMS, R .
GUT, 1973, 14 (01) :46-49
[29]  
IYANAGI T, 1991, J BIOL CHEM, V266, P24048
[30]  
IYANAGI T, 1989, J BIOL CHEM, V264, P21302