Rupture of the abdominal aorta in patients with Ehlers-Danlos syndrome

被引：19

作者：

Karkos, CD ^{[1
]}

Prasad, V ^{[1
]}

Mukhopadhyay, U ^{[1
]}

Thomson, GJL ^{[1
]}

Hearn, AR ^{[1
]}

机构：

[1] Royal Preston Hosp, Dept Surg, Preston, Lancs, England

来源：

ANNALS OF VASCULAR SURGERY | 2000年 / 14卷 / 03期

关键词：

D O I：

10.1007/s100169910047

中图分类号：

R61 [外科手术学];

学科分类号：

摘要：

Ehlers-Danlos syndrome (EDS) is a heterogenous inherited disorder of collagen synthesis. Type IV is frequently associated with major vascular catastrophes and challenges the vascular surgeon with its varied clinical presentation and the difficulty of vascular repair. Rupture of the abdominal aorta is one of the most serious complications and is associated with nearly 100% mortality rate. We describe here three patients with type IV EDS. DOI:10.1007/s100169910047.

引用

页码：274 / 277

页数：4

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