Irregular presence of abnormal prion protein in appendix in variant Creutzfeldt-Jakob disease

被引:29
作者
Joiner, S
Linehan, J
Brandner, S
Wadsworth, JDF
Collinge, J
机构
[1] UCL, MRC Pr Unit, London WC1N 3BG, England
[2] UCL, Dept Neurodegenerat Dis, Inst Neurol, London WC1N 3BG, England
基金
英国医学研究理事会;
关键词
D O I
10.1136/jnnp.73.5.597
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:597 / 598
页数:2
相关论文
共 5 条
[1]   Variant Creutzfeldt-Jakob disease [J].
Collinge, J .
LANCET, 1999, 354 (9175) :317-323
[2]   Investigation of variant Creutzfeldt-Jakob disease and other human prion diseases with tonsil biopsy samples [J].
Hill, AF ;
Butterworth, RJ ;
Joiner, S ;
Jackson, G ;
Rossor, MN ;
Thomas, DJ ;
Frosh, A ;
Tolley, N ;
Bell, JE ;
Spencer, M ;
King, A ;
Al-Sarraj, S ;
Ironside, JW ;
Lantos, PL ;
Collinge, J .
LANCET, 1999, 353 (9148) :183-189
[3]   Prion immunoreactivity in appendix before clinical onset of variant Creutzfeldt-Jakob disease [J].
Hilton, DA ;
Fathers, E ;
Edwards, P ;
Ironside, JW ;
Zajicek, J .
LANCET, 1998, 352 (9129) :703-704
[4]   Retrospective study of prion-protein accumulation in tonsil and appendix tissues [J].
Ironside, JW ;
Hilton, DA ;
Ghani, A ;
Johnston, NJ ;
Conyers, L ;
McCardle, LM ;
Best, D .
LANCET, 2000, 355 (9216) :1693-1694
[5]   Tissue distribution of protease resistant prion protein in variant Creutzfeldt-Jakob disease using a highly sensitive immunoblotting assay [J].
Wadsworth, JDF ;
Joiner, S ;
Hill, AF ;
Campbell, TA ;
Desbruslais, M ;
Luthert, PJ ;
Collinge, J .
LANCET, 2001, 358 (9277) :171-180