Properdin deficiency:: molecular basis and disease association

被引:62
作者
Fijen, CAP [1 ]
van den Bogaard, R
Schipper, M
Mannens, M
Schlesinger, M
Nordin, FG
Dankert, J
Daha, MR
Sjöholm, AG
Truedsson, L
Kuijper, EJ
机构
[1] Univ Amsterdam, Acad Med Ctr, Dept Med Microbiol, NL-1105 AZ Amsterdam, Netherlands
[2] Univ Amsterdam, Acad Med Ctr, Dept Clin Genet, NL-1105 AZ Amsterdam, Netherlands
[3] Barzilai Med Ctr, Dept Pediat, Ashkelon, Israel
[4] Malmo Univ Hosp, Wallenberg Lab, Sect Exp Cardiovasc Res, Dept Med, Malmo, Sweden
[5] Leiden Univ, Dept Nephrol, Leiden, Netherlands
[6] Univ Lund, Sect MIG, Dept Lab Med, Lund, Sweden
关键词
properdin; complement; meningococci; Neisseria meningitidis; alternative pathway;
D O I
10.1016/S0161-5890(99)00107-8
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:863 / 867
页数:5
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