Surfactant protein-B deficiency

被引:40
作者
Nogee, LM [1 ]
机构
[1] JOHNS HOPKINS UNIV,SCH MED,DEPT PEDIAT,BALTIMORE,MD 21205
关键词
D O I
10.1378/chest.111.6_Supplement.129S-a
中图分类号
R4 [临床医学];
学科分类号
1002 ; 100602 ;
摘要
引用
收藏
页码:S129 / S135
页数:7
相关论文
共 43 条
[31]   ONTOGENY OF SURFACTANT PROTEIN-A AND PROTEIN-B IN HUMAN AMNIOTIC-FLUID AS INDEXES OF FETAL LUNG MATURITY [J].
PRYHUBER, GS ;
HULL, WM ;
FINK, I ;
MCMAHAN, MJ ;
WHITSETT, JA .
PEDIATRIC RESEARCH, 1991, 30 (06) :597-605
[32]   THE USE OF SYNTHETIC PEPTIDES IN THE FORMATION OF BIOPHYSICALLY AND BIOLOGICALLY-ACTIVE PULMONARY SURFACTANTS [J].
REVAK, SD ;
MERRITT, TA ;
HALLMAN, M ;
HELDT, G ;
LAPOLLA, RJ ;
HOEY, K ;
HOUGHTEN, RA ;
COCHRANE, CG .
PEDIATRIC RESEARCH, 1991, 29 (05) :460-465
[33]   HEMATOPOIETIC AND LUNG ABNORMALITIES IN MICE WITH A NULL MUTATION OF THE COMMON BETA-SUBUNIT OF THE RECEPTORS FOR GRANULOCYTE-MACROPHAGE COLONY-STIMULATING FACTOR AND INTERLEUKIN-3 AND INTERLEUKIN-5 [J].
ROBB, L ;
DRINKWATER, CC ;
METCALF, D ;
LI, RL ;
KONTGEN, F ;
NICOLA, NA ;
BEGLEY, CG .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1995, 92 (21) :9565-9569
[34]   EXPERIMENTAL NEONATAL RESPIRATORY-FAILURE INDUCED BY A MONOCLONAL-ANTIBODY TO THE HYDROPHOBIC SURFACTANT-ASSOCIATED PROTEIN SP-B [J].
ROBERTSON, B ;
KOBAYASHI, T ;
GANZUKA, M ;
GROSSMANN, G ;
LI, WZ ;
SUZUKI, Y .
PEDIATRIC RESEARCH, 1991, 30 (03) :239-243
[35]   GRANULOCYTE/MACROPHAGE COLONY-STIMULATING FACTOR-DEFICIENT MICE SHOW NO MAJOR PERTURBATION OF HEMATOPOIESIS BUT DEVELOP A CHARACTERISTIC PULMONARY PATHOLOGY [J].
STANLEY, E ;
LIESCHKE, GJ ;
GRAIL, D ;
METCALF, D ;
HODGSON, G ;
GALL, JAM ;
MAHER, DW ;
CEBON, J ;
SINICKAS, V ;
DUNN, AR .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1994, 91 (12) :5592-5596
[36]  
VINCENT MC, 1995, HUM GENE THER, V6, P1019, DOI 10.1089/hum.1995.6.8-1019
[37]   ABERRANT PROCESSING OF SURFACTANT PROTEIN-C IN HEREDITARY SP-B DEFICIENCY [J].
VORBROKER, DK ;
PROFITT, SA ;
NOGEE, LM ;
WHITSETT, JA .
AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY, 1995, 268 (04) :L647-L656
[38]   Posttranslational processing of surfactant protein C in rat type II cells [J].
Vorbroker, DK ;
Voorhout, WF ;
Weaver, TE ;
Whitsett, JA .
AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY, 1995, 269 (06) :L727-L733
[39]   PRIMARY STRUCTURE DIFFERENCES OF HUMAN SURFACTANT-ASSOCIATED PROTEINS ISOLATED FROM NORMAL AND PROTEINOSIS LUNG [J].
VOSS, T ;
SCHAFER, KP ;
NIELSEN, PF ;
SCHAFER, A ;
MAIER, C ;
HANNAPPEL, E ;
MAASSEN, J ;
LANDIS, B ;
KLEMM, K ;
PRZYBYLSKI, M .
BIOCHIMICA ET BIOPHYSICA ACTA, 1992, 1138 (04) :261-267
[40]   FUNCTION AND REGULATION OF EXPRESSION OF PULMONARY SURFACTANT-ASSOCIATED PROTEINS [J].
WEAVER, TE ;
WHITSETT, JA .
BIOCHEMICAL JOURNAL, 1991, 273 :249-264