Cystic fibrosis transmembrane conductance regulator - Structure and function of an epithelial chloride channel

被引:99
作者
Akabas, MH
机构
[1] Columbia Univ, Dept Physiol & Cellular Biophys, Ctr Mol Recognit, New York, NY 10032 USA
[2] Columbia Univ, Dept Med, New York, NY 10032 USA
关键词
D O I
10.1074/jbc.275.6.3729
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:3729 / 3732
页数:4
相关论文
共 73 条
[1]   Channel-lining residues in the M3 membrane-spanning segment of the cystic fibrosis transmembrane conductance regulator [J].
Akabas, MH .
BIOCHEMISTRY, 1998, 37 (35) :12233-12240
[2]  
AKABAS MH, 1994, J BIOL CHEM, V269, P14865
[3]   CHLORIDE CHANNELS OF INTRACELLULAR ORGANELLES [J].
ALAWQATI, Q .
CURRENT OPINION IN CELL BIOLOGY, 1995, 7 (04) :504-508
[4]  
AMES GF, 1992, ADV ENZYMOL RAMB, V65, P1
[5]   NUCLEOSIDE TRIPHOSPHATES ARE REQUIRED TO OPEN THE CFTR CHLORIDE CHANNEL [J].
ANDERSON, MP ;
BERGER, HA ;
RICH, DP ;
GREGORY, RJ ;
SMITH, AE ;
WELSH, MJ .
CELL, 1991, 67 (04) :775-784
[6]   DEMONSTRATION THAT CFTR IS A CHLORIDE CHANNEL BY ALTERATION OF ITS ANION SELECTIVITY [J].
ANDERSON, MP ;
GREGORY, RJ ;
THOMPSON, S ;
SOUZA, DW ;
PAUL, S ;
MULLIGAN, RC ;
SMITH, AE ;
WELSH, MJ .
SCIENCE, 1991, 253 (5016) :202-205
[7]  
BERGER HA, 1993, J BIOL CHEM, V268, P2037
[8]   THE 2 NUCLEOTIDE-BINDING DOMAINS OF CYSTIC-FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR (CFTR) HAVE DISTINCT FUNCTIONS IN CONTROLLING CHANNEL ACTIVITY [J].
CARSON, MR ;
TRAVIS, SM ;
WELSH, MJ .
JOURNAL OF BIOLOGICAL CHEMISTRY, 1995, 270 (04) :1711-1717
[9]  
CHANG XB, 1993, J BIOL CHEM, V268, P11304
[10]   Locating the anion-selectivity filter of the cystic fibrosis transmembrane conductance regulator (CFTR) chloride channel [J].
Cheung, M ;
Akabas, MH .
JOURNAL OF GENERAL PHYSIOLOGY, 1997, 109 (03) :289-299