Congenital misalignment of pulmonary veins with alveolar capillary dysplasia causing persistent neonatal pulmonary hypertension: Report of two affected siblings

被引：34

作者：

Gutierrez, C

Rodriguez, A

Palenzuela, S

Forteza, C

Rossello, JLD

机构：

[1] Hosp Pereira Rossell, Pediat Pathol Lab, Montevideo 16059, Uruguay

[2] Hosp Clin Montevideo, Latin Amer Ctr Perinatol & Human Dev, Montevideo 11600, Uruguay

来源：

PEDIATRIC AND DEVELOPMENTAL PATHOLOGY | 2000年 / 3卷 / 03期

关键词：

congenital alveolar capillary dysplasia; family occurrence; misalignment of the pulmonary vessels; persistent neonatal pulmonary hypertension;

D O I：

10.1007/s100249910035

中图分类号：

R36 [病理学];

学科分类号：

100104 ;

摘要：

Misalignment of pulmonary vessels with alveolar capillary dysplasia is a rare cause of persistent pulmonary hypertension of the newborn. Most of the reported cases have been sporadic. We present two consecutive affected siblings with this disorder. This is the fifth reported family occurrence of this condition. In addition to the pulmonary abnormality, one of our cases had duodenal atresia.

引用

页码：271 / 276

页数：6

共 28 条

[1] LATE PRESENTATION OF MISALIGNMENT OF LUNG VESSELS WITH ALVEOLAR CAPILLARY DYSPLASIA [J].