共 10 条
Inactivation of the murine Transferrin receptor 2 gene using the Cre recombinase:: IoxP system
被引:8
作者:

Wallace, DF
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机构: Queensland Inst Med Res, Membrane Transport Lab, Brisbane, Qld 4006, Australia

Tonks, ID
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h-index: 0
机构: Queensland Inst Med Res, Membrane Transport Lab, Brisbane, Qld 4006, Australia

Zournazi, A
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h-index: 0
机构: Queensland Inst Med Res, Membrane Transport Lab, Brisbane, Qld 4006, Australia

Kay, GF
论文数: 0 引用数: 0
h-index: 0
机构: Queensland Inst Med Res, Membrane Transport Lab, Brisbane, Qld 4006, Australia

Subramaniam, VN
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h-index: 0
机构:
Queensland Inst Med Res, Membrane Transport Lab, Brisbane, Qld 4006, Australia Queensland Inst Med Res, Membrane Transport Lab, Brisbane, Qld 4006, Australia
机构:
[1] Queensland Inst Med Res, Membrane Transport Lab, Brisbane, Qld 4006, Australia
[2] Queensland Inst Med Res, Queensland Canc Fund Transgen Lab, Brisbane, Qld 4006, Australia
来源:
关键词:
transferrin receptor 2;
conditional knockout;
hemochromatosis;
iron homeostasis;
D O I:
10.1002/gene.20023
中图分类号:
Q [生物科学];
学科分类号:
07 ;
0710 ;
09 ;
摘要:
Transferrin Receptor 2 (TfR2) is a key molecule involved in the regulation of iron homeostasis. Mutations in TfR2 lead to type 3 hemochromatosis in humans. We have developed mice with a targeted deletion of TfR2. The Cre-recombinase:loxP system used to create the mice allows both full deletion and tissue-specific deletion of TfR2. The development of these mice will provide new models for type 3 hemochromatosis and assist in determining the role of TfR2 in iron metabolism. (C) 2004 Wiley-Liss, Inc.
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页码:38 / 41
页数:4
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