共 7 条
Huntington's disease - Making connections
被引:22
作者:

Greenamyre, J. Timothy
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Pittsburgh, Pittsburgh Inst Neurodegenerat Dis, Pittsburgh, PA 15260 USA Univ Pittsburgh, Pittsburgh Inst Neurodegenerat Dis, Pittsburgh, PA 15260 USA
机构:
[1] Univ Pittsburgh, Pittsburgh Inst Neurodegenerat Dis, Pittsburgh, PA 15260 USA
[2] Univ Pittsburgh, Dept Neurol, Pittsburgh, PA 15260 USA
关键词:
D O I:
10.1056/NEJMcibr067022
中图分类号:
R5 [内科学];
学科分类号:
1002 ;
100201 ;
摘要:
[No abstract available]
引用
收藏
页码:518 / 520
页数:3
相关论文
共 7 条
[1]
Transcriptional repression of PGC-α by mutant huntingtin leads to mitochondrial dysfunction and neurodegeneration
[J].
Cui, Libin
;
Jeong, Hyunkyung
;
Borovecki, Fran
;
Parkhurst, Christopher N.
;
Tanese, Naoko
;
Krainc, Dimitri
.
CELL,
2006, 127 (01)
:59-69

Cui, Libin
论文数: 0 引用数: 0
h-index: 0
机构:
Harvard Univ, Massachusetts Gen Hosp, Sch Med, MassGen Inst Neurodegenerat,Dept Neurol, Charlestown, MA 02129 USA Harvard Univ, Massachusetts Gen Hosp, Sch Med, MassGen Inst Neurodegenerat,Dept Neurol, Charlestown, MA 02129 USA

Jeong, Hyunkyung
论文数: 0 引用数: 0
h-index: 0
机构: Harvard Univ, Massachusetts Gen Hosp, Sch Med, MassGen Inst Neurodegenerat,Dept Neurol, Charlestown, MA 02129 USA

Borovecki, Fran
论文数: 0 引用数: 0
h-index: 0
机构: Harvard Univ, Massachusetts Gen Hosp, Sch Med, MassGen Inst Neurodegenerat,Dept Neurol, Charlestown, MA 02129 USA

Parkhurst, Christopher N.
论文数: 0 引用数: 0
h-index: 0
机构: Harvard Univ, Massachusetts Gen Hosp, Sch Med, MassGen Inst Neurodegenerat,Dept Neurol, Charlestown, MA 02129 USA

Tanese, Naoko
论文数: 0 引用数: 0
h-index: 0
机构: Harvard Univ, Massachusetts Gen Hosp, Sch Med, MassGen Inst Neurodegenerat,Dept Neurol, Charlestown, MA 02129 USA

Krainc, Dimitri
论文数: 0 引用数: 0
h-index: 0
机构: Harvard Univ, Massachusetts Gen Hosp, Sch Med, MassGen Inst Neurodegenerat,Dept Neurol, Charlestown, MA 02129 USA
[2]
The role of mitochondria in inherited neurodegenerative diseases
[J].
Kwong, Jennifer Q.
;
Beal, M. Flint
;
Manfredi, Giovanni
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JOURNAL OF NEUROCHEMISTRY,
2006, 97 (06)
:1659-1675

Kwong, Jennifer Q.
论文数: 0 引用数: 0
h-index: 0
机构:
Cornell Univ, Weill Med Coll, Dept Neurol & Neurosci, New York, NY 10021 USA Cornell Univ, Weill Med Coll, Dept Neurol & Neurosci, New York, NY 10021 USA

Beal, M. Flint
论文数: 0 引用数: 0
h-index: 0
机构:
Cornell Univ, Weill Med Coll, Dept Neurol & Neurosci, New York, NY 10021 USA Cornell Univ, Weill Med Coll, Dept Neurol & Neurosci, New York, NY 10021 USA

Manfredi, Giovanni
论文数: 0 引用数: 0
h-index: 0
机构:
Cornell Univ, Weill Med Coll, Dept Neurol & Neurosci, New York, NY 10021 USA Cornell Univ, Weill Med Coll, Dept Neurol & Neurosci, New York, NY 10021 USA
[3]
Huntingtin and the molecular pathogenesis of Huntington's disease - Fourth in molecular medicine review series
[J].
Landles, C
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Bates, GP
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EMBO REPORTS,
2004, 5 (10)
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Landles, C
论文数: 0 引用数: 0
h-index: 0
机构:
Guys Hosp, Univ London Kings Coll, GKT Sch Med, Neurogenet Lab, London SE1 9RT, England Guys Hosp, Univ London Kings Coll, GKT Sch Med, Neurogenet Lab, London SE1 9RT, England

Bates, GP
论文数: 0 引用数: 0
h-index: 0
机构:
Guys Hosp, Univ London Kings Coll, GKT Sch Med, Neurogenet Lab, London SE1 9RT, England Guys Hosp, Univ London Kings Coll, GKT Sch Med, Neurogenet Lab, London SE1 9RT, England
[4]
Peroxisome proliferator-activated receptor γ coactivator-1 promotes cardiac mitochondrial biogenesis
[J].
Lehman, JJ
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Barger, PM
;
Kovacs, A
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Saffitz, JE
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Medeiros, DM
;
Kelly, DP
.
JOURNAL OF CLINICAL INVESTIGATION,
2000, 106 (07)
:847-856

Lehman, JJ
论文数: 0 引用数: 0
h-index: 0
机构: Washington Univ, Sch Med, Dept Pathol, Cardiovasc Res Ctr, St Louis, MO 63110 USA

Barger, PM
论文数: 0 引用数: 0
h-index: 0
机构: Washington Univ, Sch Med, Dept Pathol, Cardiovasc Res Ctr, St Louis, MO 63110 USA

Kovacs, A
论文数: 0 引用数: 0
h-index: 0
机构: Washington Univ, Sch Med, Dept Pathol, Cardiovasc Res Ctr, St Louis, MO 63110 USA

Saffitz, JE
论文数: 0 引用数: 0
h-index: 0
机构: Washington Univ, Sch Med, Dept Pathol, Cardiovasc Res Ctr, St Louis, MO 63110 USA

Medeiros, DM
论文数: 0 引用数: 0
h-index: 0
机构: Washington Univ, Sch Med, Dept Pathol, Cardiovasc Res Ctr, St Louis, MO 63110 USA

Kelly, DP
论文数: 0 引用数: 0
h-index: 0
机构: Washington Univ, Sch Med, Dept Pathol, Cardiovasc Res Ctr, St Louis, MO 63110 USA
[5]
Early mitochondrial calcium defects in Huntington's disease are a direct effect of polyglutamines
[J].
Panov, AV
;
Gutekunst, CA
;
Leavitt, BR
;
Hayden, MR
;
Burke, JR
;
Strittmatter, WJ
;
Greenamyre, JT
.
NATURE NEUROSCIENCE,
2002, 5 (08)
:731-736

Panov, AV
论文数: 0 引用数: 0
h-index: 0
机构: Emory Univ, Sch Med, Dept Neurol, Atlanta, GA 30322 USA

Gutekunst, CA
论文数: 0 引用数: 0
h-index: 0
机构: Emory Univ, Sch Med, Dept Neurol, Atlanta, GA 30322 USA

Leavitt, BR
论文数: 0 引用数: 0
h-index: 0
机构: Emory Univ, Sch Med, Dept Neurol, Atlanta, GA 30322 USA

Hayden, MR
论文数: 0 引用数: 0
h-index: 0
机构: Emory Univ, Sch Med, Dept Neurol, Atlanta, GA 30322 USA

Burke, JR
论文数: 0 引用数: 0
h-index: 0
机构: Emory Univ, Sch Med, Dept Neurol, Atlanta, GA 30322 USA

Strittmatter, WJ
论文数: 0 引用数: 0
h-index: 0
机构: Emory Univ, Sch Med, Dept Neurol, Atlanta, GA 30322 USA

Greenamyre, JT
论文数: 0 引用数: 0
h-index: 0
机构: Emory Univ, Sch Med, Dept Neurol, Atlanta, GA 30322 USA
[6]
Suppression of reactive oxygen species and neurodegeneration by the PGC-1 transcriptional coactivators
[J].
St-Pierre, Julie
;
Drori, Stavit
;
Uldry, Marc
;
Silvaggi, Jessica M.
;
Rhee, James
;
Jager, Sibylle
;
Handschin, Christoph
;
Zheng, Kangni
;
Lin, Jiandie
;
Yang, Wenli
;
Simon, David K.
;
Bachoo, Robert
;
Spiegelman, Bruce M.
.
CELL,
2006, 127 (02)
:397-408

论文数: 引用数:
h-index:
机构:

Drori, Stavit
论文数: 0 引用数: 0
h-index: 0
机构: Harvard Univ, Sch Med, Dana Farber Canc Inst, Boston, MA 02115 USA

Uldry, Marc
论文数: 0 引用数: 0
h-index: 0
机构: Harvard Univ, Sch Med, Dana Farber Canc Inst, Boston, MA 02115 USA

Silvaggi, Jessica M.
论文数: 0 引用数: 0
h-index: 0
机构: Harvard Univ, Sch Med, Dana Farber Canc Inst, Boston, MA 02115 USA

Rhee, James
论文数: 0 引用数: 0
h-index: 0
机构: Harvard Univ, Sch Med, Dana Farber Canc Inst, Boston, MA 02115 USA

Jager, Sibylle
论文数: 0 引用数: 0
h-index: 0
机构: Harvard Univ, Sch Med, Dana Farber Canc Inst, Boston, MA 02115 USA

论文数: 引用数:
h-index:
机构:

Zheng, Kangni
论文数: 0 引用数: 0
h-index: 0
机构: Harvard Univ, Sch Med, Dana Farber Canc Inst, Boston, MA 02115 USA

Lin, Jiandie
论文数: 0 引用数: 0
h-index: 0
机构: Harvard Univ, Sch Med, Dana Farber Canc Inst, Boston, MA 02115 USA

Yang, Wenli
论文数: 0 引用数: 0
h-index: 0
机构: Harvard Univ, Sch Med, Dana Farber Canc Inst, Boston, MA 02115 USA

Simon, David K.
论文数: 0 引用数: 0
h-index: 0
机构: Harvard Univ, Sch Med, Dana Farber Canc Inst, Boston, MA 02115 USA

Bachoo, Robert
论文数: 0 引用数: 0
h-index: 0
机构: Harvard Univ, Sch Med, Dana Farber Canc Inst, Boston, MA 02115 USA

Spiegelman, Bruce M.
论文数: 0 引用数: 0
h-index: 0
机构: Harvard Univ, Sch Med, Dana Farber Canc Inst, Boston, MA 02115 USA
[7]
Thermoregulatory and metabolic defects in Huntington's disease transgenic mice implicate PGC-1α in Huntington's disease neurodegeneration
[J].
Weydt, Patrick
;
Pineda, Victor V.
;
Torrence, Anne E.
;
Libby, Randell T.
;
Satterfield, Terrence F.
;
Lazarowski, Eduardo R.
;
Gilbert, Merle L.
;
Morton, Gregory J.
;
Bammler, Theodor K.
;
Strand, Andrew D.
;
Cui, Libin
;
Beyer, Richard P.
;
Easley, Courtney N.
;
Smith, Annette C.
;
Krainc, Dimitri
;
Luquet, Serge
;
Sweet, Ian R.
;
Schwartz, Michael W.
;
La Spada, Albert R.
.
CELL METABOLISM,
2006, 4 (05)
:349-362

Weydt, Patrick
论文数: 0 引用数: 0
h-index: 0
机构: Univ Washington, Ctr Neurogenet & Neurotherapeut, Dept Lab Med, Seattle, WA 98195 USA

Pineda, Victor V.
论文数: 0 引用数: 0
h-index: 0
机构: Univ Washington, Ctr Neurogenet & Neurotherapeut, Dept Lab Med, Seattle, WA 98195 USA

Torrence, Anne E.
论文数: 0 引用数: 0
h-index: 0
机构: Univ Washington, Ctr Neurogenet & Neurotherapeut, Dept Lab Med, Seattle, WA 98195 USA

Libby, Randell T.
论文数: 0 引用数: 0
h-index: 0
机构: Univ Washington, Ctr Neurogenet & Neurotherapeut, Dept Lab Med, Seattle, WA 98195 USA

Satterfield, Terrence F.
论文数: 0 引用数: 0
h-index: 0
机构: Univ Washington, Ctr Neurogenet & Neurotherapeut, Dept Lab Med, Seattle, WA 98195 USA

Lazarowski, Eduardo R.
论文数: 0 引用数: 0
h-index: 0
机构: Univ Washington, Ctr Neurogenet & Neurotherapeut, Dept Lab Med, Seattle, WA 98195 USA

Gilbert, Merle L.
论文数: 0 引用数: 0
h-index: 0
机构: Univ Washington, Ctr Neurogenet & Neurotherapeut, Dept Lab Med, Seattle, WA 98195 USA

Morton, Gregory J.
论文数: 0 引用数: 0
h-index: 0
机构: Univ Washington, Ctr Neurogenet & Neurotherapeut, Dept Lab Med, Seattle, WA 98195 USA

Bammler, Theodor K.
论文数: 0 引用数: 0
h-index: 0
机构: Univ Washington, Ctr Neurogenet & Neurotherapeut, Dept Lab Med, Seattle, WA 98195 USA

Strand, Andrew D.
论文数: 0 引用数: 0
h-index: 0
机构: Univ Washington, Ctr Neurogenet & Neurotherapeut, Dept Lab Med, Seattle, WA 98195 USA

Cui, Libin
论文数: 0 引用数: 0
h-index: 0
机构: Univ Washington, Ctr Neurogenet & Neurotherapeut, Dept Lab Med, Seattle, WA 98195 USA

Beyer, Richard P.
论文数: 0 引用数: 0
h-index: 0
机构: Univ Washington, Ctr Neurogenet & Neurotherapeut, Dept Lab Med, Seattle, WA 98195 USA

Easley, Courtney N.
论文数: 0 引用数: 0
h-index: 0
机构: Univ Washington, Ctr Neurogenet & Neurotherapeut, Dept Lab Med, Seattle, WA 98195 USA

Smith, Annette C.
论文数: 0 引用数: 0
h-index: 0
机构: Univ Washington, Ctr Neurogenet & Neurotherapeut, Dept Lab Med, Seattle, WA 98195 USA

Krainc, Dimitri
论文数: 0 引用数: 0
h-index: 0
机构: Univ Washington, Ctr Neurogenet & Neurotherapeut, Dept Lab Med, Seattle, WA 98195 USA

Luquet, Serge
论文数: 0 引用数: 0
h-index: 0
机构: Univ Washington, Ctr Neurogenet & Neurotherapeut, Dept Lab Med, Seattle, WA 98195 USA

Sweet, Ian R.
论文数: 0 引用数: 0
h-index: 0
机构: Univ Washington, Ctr Neurogenet & Neurotherapeut, Dept Lab Med, Seattle, WA 98195 USA

Schwartz, Michael W.
论文数: 0 引用数: 0
h-index: 0
机构: Univ Washington, Ctr Neurogenet & Neurotherapeut, Dept Lab Med, Seattle, WA 98195 USA

La Spada, Albert R.
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Washington, Ctr Neurogenet & Neurotherapeut, Dept Lab Med, Seattle, WA 98195 USA Univ Washington, Ctr Neurogenet & Neurotherapeut, Dept Lab Med, Seattle, WA 98195 USA