Alpha-1-antitrypsin replacement therapy: will its efficacy ever be proved?

被引:20
作者
Hutchison, DCS [1 ]
Hughes, MD [1 ]
机构
[1] UNIV LONDON LONDON SCH HYG & TROP MED, DEPT EPIDEMIOL & POPULAT HLTH, MED STAT UNIT, LONDON WC1E 7HT, ENGLAND
关键词
D O I
10.1183/09031936.97.10102191
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
引用
收藏
页码:2191 / 2193
页数:3
相关论文
共 19 条
[1]   CLINICAL-FEATURES AND HISTORY OF THE DESTRUCTIVE LUNG-DISEASE ASSOCIATED WITH ALPHA-1-ANTITRYPSIN DEFICIENCY OF ADULTS WITH PULMONARY SYMPTOMS [J].
BRANTLY, ML ;
PAUL, LD ;
MILLER, BH ;
FALK, RT ;
WU, M ;
CRYSTAL, RG .
AMERICAN REVIEW OF RESPIRATORY DISEASE, 1988, 138 (02) :327-336
[2]   BIOCHEMICAL AND BIOLOGICAL PROPERTIES OF AN ALPHA-1-ANTITRYPSIN CONCENTRATE [J].
BURNOUF, T ;
CONSTANS, J ;
CLERC, A ;
DESCAMPS, J ;
MARTINACHE, L ;
GOUDEMAND, M .
VOX SANGUINIS, 1987, 52 (04) :291-297
[3]  
BURROWS B, 1983, AM REV RESPIR DIS, V127, pS42
[4]  
COAN M H, 1990, European Respiratory Journal, V3, p35S
[5]   DECLINE IN PULMONARY-FUNCTION IN PATIENTS WITH ALPHA-1-ANTITRYPSIN DEFICIENCY [J].
EVALD, T ;
DIRKSEN, A ;
KEITTELMANN, S ;
VISKUM, K ;
KOKJENSEN, A .
LUNG, 1990, 168 :579-585
[6]  
GADEK JE, 1983, AM REV RESPIR DIS, V127, pS45
[7]   REPLACEMENT THERAPY OF ALPHA-1-ANTITRYPSIN DEFICIENCY - REVERSAL OF PROTEASE-ANTIPROTEASE IMBALANCE WITHIN THE ALVEOLAR STRUCTURES OF PIZ SUBJECTS [J].
GADEK, JE ;
KLEIN, HG ;
HOLLAND, PV ;
CRYSTAL, RG .
JOURNAL OF CLINICAL INVESTIGATION, 1981, 68 (05) :1158-1165
[8]  
HEIN R H, 1990, European Respiratory Journal, V3, p16S
[9]   MEDICAL ETHICS AND CONTROLLED TRIALS [J].
HILL, AB .
BMJ-BRITISH MEDICAL JOURNAL, 1963, (533) :1043-+
[10]  
HUBBARD RC, 1988, AM J MED, V84, P52