Dermatofibrosarcoma protuberans in childhood

Dermatofibrosarcoma protuberans (DFSP) is a rare cutaneous tumor with a possibly misleading presentation, It is rare in childhood, We report an 18-month-old child with an acquired atrophic plaque of the left ankle, Based on clinical findings, initial proposed diagnoses included localized scleroderma and localized lipoatrophy, At the age of 5 years the plaque had increased in size and become a purplish color, Several firm nodules were seen at its periphery. A diagnosis of DFSP was proposed and confirmed histologically. A large surgical resection was performed, This case illustrates that DFSP may occur in childhood, during which initial diagnosis is generally more difficult than in adulthood.