Dilated cardiomyopathy in the ectodermal dysplasia.: Electro-echocardiographic observations in palmo-plantar keratoderma with woolly hair

被引:12
作者
Durán, M
Avellán, F
Carvajal, L
机构
[1] Hosp Ninos Alejandro Mann, Dept Cardiol, Guayaquil, Ecuador
[2] Hosp Luis Vemaza, Dept Dermatol, Guayaquil, Ecuador
来源
REVISTA ESPANOLA DE CARDIOLOGIA | 2000年 / 53卷 / 09期
关键词
cardiomyopathy; echocardiography; arrhythmias;
D O I
10.1016/S0300-8932(00)75233-X
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Familial palmoplantar keratosis has not been associated with cardiac abnormalities, however, when this ectodermal dysplasia included hair shaft dystrophy a close association with cardiomyopathy was noted. We report here three family with six members in whom palmoplantar keratoderma with woolly hair and cardiac lesions was observed.
引用
收藏
页码:1296 / 1300
页数:5
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