Epidermolysis bullosa: directions for future research and new challenges for treatment

被引:9
作者
Sawamura, D [1 ]
McMillan, JR [1 ]
Akiyama, M [1 ]
Shimizu, H [1 ]
机构
[1] Hokkaido Univ, Grad Sch Med, Dept Dermatol, Kita Ku, Sapporo, Hokkaido 0608638, Japan
关键词
prenatal diagnosis; gene therapy; classification;
D O I
10.1007/s00403-002-0370-7
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
[No abstract available]
引用
收藏
页码:S34 / S42
页数:9
相关论文
共 81 条
[1]   CHARACTERIZATION OF HAIR FOLLICLE BULGE IN HUMAN FETAL SKIN - THE HUMAN FETAL BULGE IS A POOL OF UNDIFFERENTIATED KERATINOCYTES [J].
AKIYAMA, M ;
DALE, BA ;
SUN, TT ;
HOLBROOK, KA .
JOURNAL OF INVESTIGATIVE DERMATOLOGY, 1995, 105 (06) :844-850
[2]  
[Anonymous], ADV LIPID METHODOLOG
[3]   Focal activation of a mutant allele defines the role of stem cells in mosaic skin disorders [J].
Arin, MJ ;
Longley, MA ;
Wang, XJ ;
Roop, DR .
JOURNAL OF CELL BIOLOGY, 2001, 152 (03) :645-649
[4]   α6β4 integrin abnormalities in junctional epidermolysis bullosa with pyloric atresia [J].
Ashton, GHS ;
Sorelli, P ;
Mellerio, JE ;
Keane, FM ;
Eady, RAJ ;
McGrath, JA .
BRITISH JOURNAL OF DERMATOLOGY, 2001, 144 (02) :408-414
[5]   Constitutive expression of phVEGF165 after intramuscular gene transfer promotes collateral vessel development in patients with critical limb ischemia [J].
Baumgartner, I ;
Pieczek, A ;
Manor, O ;
Blair, R ;
Kearney, M ;
Walsh, K ;
Isner, JM .
CIRCULATION, 1998, 97 (12) :1114-1123
[6]   Biology of anchoring fibrils:: lessons from dystrophic epidermolysis bullosa [J].
Bruckner-Tuderman, L ;
Höpfner, B ;
Hammami-Hauasli, N .
MATRIX BIOLOGY, 1999, 18 (01) :43-54
[7]   THE STRUCTURE OF TYPE-VII COLLAGEN [J].
BURGESON, RE ;
MORRIS, NP ;
MURRAY, LW ;
DUNCAN, KG ;
KEENE, DR ;
SAKAI, LY .
ANNALS OF THE NEW YORK ACADEMY OF SCIENCES, 1985, 460 :47-57
[8]   An inducible mouse model for epidermolysis bullosa simplex: Implications for gene therapy [J].
Cao, TY ;
Longley, MA ;
Wang, XJ ;
Roop, DR .
JOURNAL OF CELL BIOLOGY, 2001, 152 (03) :651-656
[9]   PATIENTS WITH SEVERE FORMS OF INHERITED EPIDERMOLYSIS-BULLOSA EXHIBIT DECREASED LYMPHOKINE AND MONOKINE PRODUCTION [J].
CHOPRA, V ;
TYRING, SK ;
JOHNSON, L ;
FINE, JD .
JOURNAL OF CLINICAL IMMUNOLOGY, 1990, 10 (06) :321-329
[10]   Preimplantation genetic diagnosis in two families at risk for recurrence of Herlitz junctional epidermolysis bullosa [J].
Cserhalmi-Friedman, PB ;
Tang, Y ;
Adler, A ;
Krey, L ;
Grifo, JA ;
Christiano, AM .
EXPERIMENTAL DERMATOLOGY, 2000, 9 (04) :290-297