Protein-losing enteropathy after Fontan surgery: Resolution after cardiac transplantation

被引：25

作者：

Brancaccio, G ^{[1
]}

Carotti, A ^{[1
]}

D'Argenio, P ^{[1
]}

Michielon, G ^{[1
]}

Parisi, F ^{[1
]}

机构：

[1] Hosp Bambino Gesu, Cardiac Pediat Surg Dept, Rome, Italy

来源：

JOURNAL OF HEART AND LUNG TRANSPLANTATION | 2003年 / 22卷 / 04期

关键词：

D O I：

10.1016/S1053-2498(02)01231-7

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Protein-losing enteropathy (PLE), defined as severe loss of serum protein into the intestine, occurs in 4% to 13% of patients after the Fontan procedure. We report a case of PLE reversal after heart transplantation in a 14-year-old boy with Fontan circulation who previously was treated unsuccessfully with medical therapy. The protein loss continued after heart transplantation. We administered total parenteral nutrition to rest the bowel. After 16 months, we observed a gradual,decrease in protein loss. The patient is doing well 5 years after heart transplantation and had has a normal serum albumin level.

引用

页码：484 / 486

页数：3

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