Rhabdomyosarcoma - Biology and treatment

被引:58
作者
Pappo, AS [1 ]
Shapiro, DN [1 ]
Crist, WM [1 ]
机构
[1] UNIV TENNESSEE, CTR HLTH SCI, COLL MED, DEPT PEDIAT, MEMPHIS, TN 38163 USA
关键词
D O I
10.1016/S0031-3955(05)70539-3
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Rhabdomyosarcoma is the most common soft-tissue sarcoma of childhood. Recognition of specific genetic changes in the two most common subtypes of rhabdomyosarcoma has allowed better understanding of the pathogenesis of this disease. In addition, identification of prognostic factors and the use of risk-directed multimodal therapy have improved the outcome for these patients significantly, with cure rates approaching 70%.
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页码:953 / +
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