IS THERE A MECHANISM FOR INTRODUCING ACID-HYDROLASES INTO LIVER LYSOSOMES THAT IS INDEPENDENT OF MANNOSE 6-PHOSPHATE RECOGNITION - EVIDENCE FROM I-CELL DISEASE

被引：167

作者：

OWADA, M ^{[1
]}

NEUFELD, EF ^{[1
]}

机构：

[1] NIADDKD,GENET & BIOCHEM BRANCH,BETHESDA,MD 20205

来源：

BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS | 1982年 / 105卷 / 03期

关键词：

D O I：

10.1016/0006-291X(82)91042-7

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：814 / 820

页数：7

共 24 条

[1] ULTRASTRUCTURAL STUDIES IN FETAL I-CELL DISEASE
ABE, K
MATSUDA, I
ARASHIMA, S
MITSUYAMA, T
OKA, Y
ISHIKAWA, M
[J]. PEDIATRIC RESEARCH, 1976, 10 (07) : 669 - 676
[2] I-CELL DISEASE - DEFICIENCY OF EXTRACELLULAR HYDROLASE PHOSPHORYLATION
BACH, G
BARGAL, R
CANTZ, M
[J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1979, 91 (03) : 976 - 981
[3] I-CELL DISEASE, MUCOLIPIDOSIS .2. PATHOLOGICAL, HISTOCHEMICAL, ULTRASTRUCTURAL AND BIOCHEMICAL OBSERVATIONS IN 4 CASES
GILBERT, EF
DAWSON, G
RHEIN, GMZ
OPITZ, JM
SPRANGER, JW
[J]. ZEITSCHRIFT FUR KINDERHEILKUNDE, 1973, 114 (04): : 259 - 292
[4] ENZYMATIC PHOSPHORYLATION OF LYSOSOMAL-ENZYMES IN THE PRESENCE OF UDP-N-ACETYLGLUCOSAMINE - ABSENCE OF THE ACTIVITY IN I-CELL FIBROBLASTS
HASILIK, A
WAHEED, A
VONFIGURA, K
[J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1981, 98 (03) : 761 - 767
[5] HASILIK A, 1980, J BIOL CHEM, V255, P4946
[6] HASILIK A, 1980, J BIOL CHEM, V255, P4937
[7] ISOELECTRIC-FOCUSING OF ACID-HYDROLASES IN HUMAN LIVER AND SERUM - FINDINGS IN SERA FROM ONE PATIENT WITH I-CELL DISEASE PHENOTYPE
HULTBERG, B
[J]. CLINICA CHIMICA ACTA, 1978, 88 (03) : 441 - 448
[8] PHOSPHOHEXOSYL COMPONENTS OF A LYSOSOMAL ENZYME ARE RECOGNIZED BY PINOCYTOSIS RECEPTORS ON HUMAN FIBROBLASTS
KAPLAN, A
ACHORD, DT
SLY, WS
[J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1977, 74 (05) : 2026 - 2030
[9] HEPATIC ULTRASTRUCTURE AND HISTOCHEMISTRY IN MUCOLIPIDOSIS-II (I-CELL DISEASE)
KENYON, KR
SENSENBRENNER, JA
WYLLIE, RG
[J]. PEDIATRIC RESEARCH, 1973, 7 (06) : 560 - 568
[10] I-CELL DISEASE (MUCOLIPIDOSIS-II) - REPORT ON ITS PATHOLOGY
MARTIN, JJ
LEROY, JG
FARRIAUX, JP
FONTAINE, G
DESNICK, RJ
CABELLO, A
[J]. ACTA NEUROPATHOLOGICA, 1975, 33 (04) : 285 - 305

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