SERUM NEUTRAL ALPHA-D-GLUCOSIDASE FROM PATIENTS WITH CYSTIC-FIBROSIS AND CHRONIC PULMONARY-DISEASE

被引:1
作者
ALHADEFF, JA [1 ]
POLLACK, BC [1 ]
HOPFER, RL [1 ]
HOLSCLAW, DS [1 ]
机构
[1] HAHNEMANN UNIV,DEPT PEDIAT,PHILADELPHIA,PA 19102
关键词
D O I
10.1203/00006450-198502000-00004
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:171 / 174
页数:4
相关论文
共 9 条
[1]   ACTIVITY LEVELS AND PROPERTIES OF ACID ALPHA-GLUCOSIDASE FROM LIVER AND NEUTRAL ALPHA-GLUCOSIDASE FROM SERA OF CYSTIC-FIBROSIS PATIENTS AND CONTROLS [J].
ALHADEFF, JA ;
THOM, D ;
HOLZINGER, RT .
CLINICA CHIMICA ACTA, 1981, 117 (02) :227-237
[2]  
ALHADEFF JA, 1980, PERSPECTIVES CYSTIC, P35
[3]   CYSTIC-FIBROSIS - LYSOSOMAL AND MITOCHONDRIAL ENZYME-ACTIVITIES OF LYMPHOID-CELL LINES [J].
ANTONOWICZ, I ;
SIPPELL, WG ;
SHWACHMAN, H .
PEDIATRIC RESEARCH, 1972, 6 (11) :803-+
[4]   GLYCOSIDASES IN SERUM OF CYSTIC-FIBROSIS PATIENTS [J].
CASOLA, L ;
DIMATTEO, G ;
ROMANO, M ;
RUTIGLIANO, B ;
MASTELLA, G .
CLINICA CHIMICA ACTA, 1979, 94 (01) :83-88
[5]  
Di Matteo G, 1979, Monogr Paediatr, V10, P19
[6]   CYSTIC-FIBROSIS - LEAKAGE OF LYSOSOMAL ENZYMES AND OF ALKALINE-PHOSPHATASE INTO EXTRACELLULAR-SPACE [J].
HOSLI, P ;
VOGT, E .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1977, 79 (03) :741-748
[7]  
RIORDAN JR, 1980, PERSPECTIVES CYSTIC, P313
[8]   LONG-TERM STUDY OF 105 PATIENTS WITH CYSTIC FIBROSIS [J].
SHWACHMAN, H ;
KULCZYCKI, LL .
AMA JOURNAL OF DISEASES OF CHILDREN, 1958, 96 (01) :6-15
[9]  
TALAMO RC, 1983, METABOLIC BASIS INHE, P1889