THE OMENNS SYNDROME - HISTOLOGICAL, IMMUNOHISTOCHEMICAL AND ULTRASTRUCTURAL EVIDENCE FOR A PARTIAL T-CELL DEFICIENCY EVOLVING IN AN ABNORMAL PROLIFERATION OF LYMPHOCYTES-T AND S-100+/T-6+ LANGERHANS-LIKE CELLS

被引:30
作者
RUCO, LP
STOPPACCIARO, A
PEZZELLA, F
MIROLO, M
UCCINI, S
BARSOTTI, P
CASSANO, AM
BONER, AL
BUSINCO, L
DIFAZIO, A
BARONI, CD
机构
[1] UNIV LA SAPIENZA,SCH MED,DEPT HUMAN BIOPATHOL,IMMUNOPATHOL SECT,CHAIR PATHOL ANAT 4,I-00161 ROME,ITALY
[2] UNIV LA SAPIENZA,SCH MED,DEPT HUMAN BIOPATHOL,ULTRASTRUCT PATHOL SECT,I-00161 ROME,ITALY
[3] UNIV LA SAPIENZA,SCH MED,DEPT PEDIAT,I-00161 ROME,ITALY
[4] BORGO ROMA HOSP,DEPT PEDIAT,I-37134 VERONA,ITALY
关键词
D O I
10.1007/BF00701330
中图分类号
R602 [外科病理学、解剖学]; R32 [人体形态学];
学科分类号
100101 ;
摘要
引用
收藏
页码:69 / 82
页数:14
相关论文
共 22 条
[1]   LYMPHOPROLIFERATION FOLLOWING ANTIGENIC-STIMULATION IN SEVERE COMBINED IMMUNODEFICIENCY DISEASE [J].
AKHTER, J ;
KRANTMAN, HJ ;
HOPPER, J ;
ROTHBERG, RM .
CLINICAL IMMUNOLOGY AND IMMUNOPATHOLOGY, 1981, 20 (03) :361-372
[2]  
ANDERSON MG, 1984, LANCET, V1, P880
[3]  
ASMA GEM, 1983, CLIN EXP IMMUNOL, V53, P429
[4]  
BARTH RF, 1972, LANCET, P503
[5]   HISTIOCYTOSIS X-CELLS AND LANGERHANS CELLS - ENZYME HISTOCHEMICAL AND IMMUNOLOGICAL SIMILARITIES [J].
BECKSTEAD, JH ;
WOOD, GS ;
TURNER, RR .
HUMAN PATHOLOGY, 1984, 15 (09) :826-833
[6]  
BUCKLEY RH, 1972, PEDIATRICS, V49, P59
[7]  
BUSINCO L, 1979, ALLERGOL IMMUNOPATH, V7, P445
[8]   REACTIVITY OF LANGERHANS CELLS WITH HYBRIDOMA ANTIBODY [J].
FITHIAN, E ;
KUNG, P ;
GOLDSTEIN, G ;
RUBENFELD, M ;
FENOGLIO, C ;
EDELSON, R .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1981, 78 (04) :2541-2544
[9]  
GROSSEYE S, 1983, CLIN IMMUNOL IMMUNOP, V29, P58
[10]  
GYORKEY F, 1971, LANCET, V1, P131